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Journals / Muğla Sıtkı Koçman Üniversitesi Tıp Dergisi / 2018 / Volume: 5 Issue: 3

Co-existence of Primary Localized Cutaneous Amyloidosis and Diffuse Systemic Sclerosis: Case Report

Primer Lokalize Kutanöz Amiloidoz ve Diffüz Sistemik Skleroz Birlikteliği: Olgu Sunumu

Emine Figen Tarhan(Muğla Sıtkı Koçman Üniversitesi Tıp Fakültesi İç hastalıkları Anabilim Dalı/Romatoloji Bilim Dalı, Muğla)0000-0002-2592-1741
Emine Koca(Muğla Sıtkı Koçman Üniversitesi Tıp Fakültesi İç hastalıkları Anabilim Dalı, Muğla)0000-0001-6607-5652
Pages
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Publication Date
2018-12-04
DOI
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

These two autoimmune diseases, which have different aetiopathogenesis as well as diverse clinical and genetic characteristics, are rarely seen together.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Co-existence of primary localized cutaneous amyloidosis and diffuse systemic sclerosis is very rare.
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Key Findings & Data:In a 61-year-old woman who was diagnosed as primary localized cutaneous amyloidosis with biopsy 15 years ago, additional diagnosis of diffuse systemic sclerosis was made based upon skin, locomotor system and capilloroscopy findings and autoantibody (anti- Scl70) positivity.
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Conclusion & Impact:These two autoimmune diseases, which have different aetiopathogenesis as well as diverse clinical and genetic characteristics, are rarely seen together.
🔬Design:Case Report
📍Scope:Comprehensive Sample
⚙️Variables:Amyloidosis · CREST · Systemic Sclerosis

Abstract

Co-existence of primary localized cutaneous amyloidosis and diffuse systemic sclerosis is very rare. In a 61-year-old woman who was diagnosed as primary localized cutaneous amyloidosis with biopsy 15 years ago, additional diagnosis of diffuse systemic sclerosis was made based upon skin, locomotor system and capilloroscopy findings and autoantibody (anti- Scl70) positivity. These two autoimmune diseases, which have different aetiopathogenesis as well as diverse clinical and genetic characteristics, are rarely seen together.

Özet

Primer lokalize kutanöz amiloidoz ve diffüz sistemik skleroz birlikteliği nadirdir. 15 yıl önce biyopsi ile primer lokalize kutanöz amiloidoz tanısı alan 61 yaşındaki bir kadın hastaya deri ve lokomotor sistem bulguları, kapilleroskopi bulguları ve otoantikor (anti-Scl-70) pozitifliği ile diffüz sistemik skleroz tanısı konulmuştur. Farklı klinik, etiyopatogenetik ve genetik özellikleri olan bu iki hastalık nadiren bir arada görülmektedir.

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Cite This Article

Tarhan, E. F., Koca, E. (2018). Co-existence of Primary Localized Cutaneous Amyloidosis and Diffuse Systemic Sclerosis: Case Report. Muğla Sıtkı Koçman Üniversitesi Tıp Dergisi, Volume: 5 Issue: 3. https://ajindex.com/articles/1294500

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