In our study 6 patients with renal amyloidosis who were managed in the Pediatric Department of Haydarpaşa Numune Hospital between years 1990 and 1998 were evaluated retrospectively Four of them 66 6 demostrated phenotype 1 characteristics of Familial Mediterranean Fever while the others 33 4 phenotype 2 characteristics In phenotype 1 subjects amyloidosis developed in a period from 3 to 9 years after the onset periodic attacks Three of four patients who had renal failure died in one year period Key words: renal amyloidosis familial Mediterranean fever
📌 3 Key Takeaways
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Objective & Hypothesis:In our study 6 patients with renal amyloidosis who were managed in the Pediatric Department of Haydarpaşa Numune Hospital between years 1990 and 1998 were evaluated retrospectively Four of them 66 6 demostrated phenotype 1 characteristics of Familial Mediterranean Fever while the others 33 4 phenotype 2 characteristics In phenotype 1 subjects amyloidosis developed in a period from 3 to 9 years after the onset periodic attacks Three of four patients who had renal failure died in one year period Key words: renal amyloidosis familial Mediterranean fever
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Key Findings & Data:In our study 6 patients with renal amyloidosis who were managed in the Pediatric Department of Haydarpaşa Numune Hospital between years 1990 and 1998 were evaluated retrospectively Four of them 66 6 demostrated phenotype 1 characteristics of Familial Mediterranean Fever while the others 33 4 phenotype 2 characteristics In phenotype 1 subjects amyloidosis developed in a period from 3 to 9 years after the onset periodic attacks Three of four patients who had renal failure died in one year period Key words: renal amyloidosis familial Mediterranean fever
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Conclusion & Impact:In our study 6 patients with renal amyloidosis who were managed in the Pediatric Department of Haydarpaşa Numune Hospital between years 1990 and 1998 were evaluated retrospectively Four of them 66 6 demostrated phenotype 1 characteristics of Familial Mediterranean Fever while the others 33 4 phenotype 2 characteristics In phenotype 1 subjects amyloidosis developed in a period from 3 to 9 years after the onset periodic attacks Three of four patients who had renal failure died in one year period Key words: renal amyloidosis familial Mediterranean fever
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters
Abstract
In our study 6 patients with renal amyloidosis who were managed in the Pediatric Department of Haydarpaşa Numune Hospital between years 1990 and 1998 were evaluated retrospectively Four of them 66 6 demostrated phenotype 1 characteristics of Familial Mediterranean Fever while the others 33 4 phenotype 2 characteristics In phenotype 1 subjects amyloidosis developed in a period from 3 to 9 years after the onset periodic attacks Three of four patients who had renal failure died in one year period Key words: renal amyloidosis familial Mediterranean fever
Özet
1990 1998 yılları arasında Haydarpaşa Numune Hastanesi Çocuk Sağlığı ve Hastalıkları Kliniği’nde yatırılarak izlenen yaşları 7 13 yaş arası olan 3 kız 3 erkek renal amiloidozlu olgu klinik ve laboratuvar bulguları açısından incelenmiştir 4 hasta 66 6 ailevi Akdeniz ateşi Fenotip 1’in özelliklerini gösterirken 2’si 33 4 Fenotip 2 ile uyumluydu Fenotip 1’li vakalarda renal amiloidoz periodik ataklardan 3 9 yıl sonra gelişmişti Böbrek yetersizliği gelişen 4 olgudan 3’ü bir yıl içinde exitus oldu Anahtar Kelimeler: renal amiloidoz ailevi Akdeniz ateşi
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Cite This Article
Narter, F. K., Yavrucu, S., Kıral, A., Özer, I. (2002). Six patients with renal amyloidosis secondary to familial Mediterranean fever Original Article. Türk Pediatri Arşivi, Cilt: 37 Sayı: 4, 1–1. https://ajindex.com/articles/1012270