Paget’s Disease of Vulva: A case report

Abstract

Extramammary Paget’s disease (EMPD) is a rare clinical entity which can be associated with other malignancies. The vulva is the mostly seen presentation in women. Lesions frequently presents in adnexal structures and clinically demonstrate as erythematous, well-demarcated plaques. Early detection is mandatory because the diagnosis is frequently delayed and there is a high incidence of associated invasive disease. With this case, we discuss the management of vulvar Paget's disease which is rarely seen and importance of investigating the accompanying secondary malignancies.