Dergiler / Zeynep Kamil Tıp Bülteni / 2014 / Cilt: 45 - Sayı: 3
Uterusun İntravasküler Lipoleiomyomatozisi (Intravenous Lipoleiomyomatosis of Uterus: a Rare Subtype of Intravenous Leiomyomatosis)
- Sayfa
- 113–115
- DOI
- —
Özet
Lipoleiomyomatozis (LPL) dikkat çekici miktarda yağ dokusu içeren leiomyomlardır. Intravenöz LPL ise intravenöz leiomyomatozisin (IVL) nadir görülen bir alt tipidir. IVL benign bir lezyon olarak tanımlanmasına rağmen, IVL olarak bildirilen olguların %10'unda rekürrens saptanmıştır. Aynı zamanda mutlaka low-grade endometrial stromal sarkom ve vasküler invazyon yapan leiomyosarkomdan ayrımı yapılmalıdır. Hastanemizde myom nedeniyle opere edilmiş ve kliniğimizde myometriuma sınırlı intravenöz LPL tanısı alan olgumuzu literatür eşliğinde sunduk. Anahtar kelimeler: intravasküler leiomyom, intravenöz lipoleiomyomatozis, leiomyom.Abstract Lipoleiomyomatosis (LPL) is a rare benign tumor composed of fat and smooth muscle. Intravenous LPL is a rare subtype of intravenous leiomyomatosis (IVL). Although LPL is considered to be a benign lesion, IVL recurs in approximately 10% of reported cases, and must be distinguished from low-grade endometrial stromal sarcoma and leiomyosarcoma with vascular invasion. We report a case of intravenous LPL in the light of literature as a diagnostic challenge.Key words: intravenous leiomyomatosis, intravenous lipoleiomyomatosis, leiomyoma.
Abstract
Lipoleiomyomatosis (LPL) is a rare benign tumor composed of fat and smooth muscle. Intravenous LPL is a rare subtype of intravenous leiomyomatosis (IVL). Although LPL is considered to be a benign lesion, IVL recurs in approximately 10% of reported cases, and must be distinguished from low-grade endometrial stromal sarcoma and leiomyosarcoma with vascular invasion. We report a case of intravenous LPL in the light of literature as a diagnostic challenge.