Teratoid Wilms Tumor: Report of Three Cases and Review of the Literature

Abstract

Teratoid Wilms tumor is a rare variant of Wilms tumor composed predominantly of well-differentiated epithelial and/or mesenchymalheterologous elements. Like the classical Wilms tumor, this variant may also occur as a renal mass or may be found in extra renal locations. Thistumor may be treated effectively by surgical resection; however, it generally fails to respond to chemotherapy. A review of the literature revealed30 reported cases of intra renal and 5 reports of extra renal teratoid Wilms tumor. We report our experience with an additional three cases ofrenal teratoid Wilms tumor adding to the 30 cases previously reported.