Pediatric Tonsillar Synovial Sarcoma- Very Rare Localization: A Case Report and Review of the Literature

Abstract

Tonsillar synovial sarcoma is an extremely rare entity and only 9 adult patients have been reported up to now. Here, we describe the first pediatrictonsillar synovial sarcoma of the literature in a patient who presented with a 2-month history of dysphagia and snoring. Clinical and radiologicalexaminations showed that the tumor arose from the right palatine tonsil and narrowed the parapharyngeal space. An incisional biopsy fromthe palatine tonsil revealed the diagnosis of synovial sarcoma. The patient has underwent total tonsillectomy and received radiotherapy andchemotherapy because of the positive surgical margins. The patient is clinically in good condition and free of tumor 30 months after the initialdiagnosis. We achieved a long-term complete remission with a combination of surgery, radiotherapy and chemotherapy in our case. Tonsillarsynovial sarcoma should be kept in mind while dealing with tonsillar masses. We can conclude that a multidisciplinary approach is warrantedwhile treating synovial sarcoma with this localization.