A Rare Cause of Recurrent Spontaneous Pneumothorax: Birt-Hogg-Dube Syndrome

Özet

Birt-Hogg-Dube (BHD) syndrome is an unusual disorder characterized by the triad of cutaneous lesions, renal tumors and lung cysts. Incases with BHD syndrome, the frequency of recurrent pneumothorax is increased due to presence of multiple lung cysts. It is importantto evaluate the BHD syndrome in differential diagnosis of recurrent pneumothorax especially with multiple lung cysts predominating inthe lung base. In these patients, the presence of accompanying kidney and other tumors should be investigated. Herein, we report a caseof BHD syndrome presenting with recurrent pneumothorax.