Lumbosacral Epidural Primitive Neuroectodermal Tumor (PNET): Case Report and Literature Review

Özet

The primitive neuroectodermal tumors (PNETs) of the spine are rare. They are usually intramedullary and reported in children.We herein report an epidural PNET of lumbosacral area presenting with the cauda equina syndrome in an adult. A 38-year-oldwoman presented to our emergency room with acute onset lower extremity weakness and urinary incontinence. Emergent magneticresonance imaging revealed a mass lesion isointense on T1-weighted and heterogeneously hyperintense in T2-weighted imagesin the epidural lumbosacral area. The patient underwent emergent laminectomy of L1-L3 and total resection of the lesion. Thepatient’s neurological examination improved dramatically after the surgery and after 6-month of follow-up, she was neurologicallyintact. The histopathological and immunohistochemical evaluations revealed PNET. Epidural PNET of the spinal column, althoughrare, can present with an acute neurological deficit. Surgery remains the treatment of choice and immunohistochemistry is requiredfor confirming the diagnosis.