Dergiler / Turkish Journal of Hematology / 2000 / Cilt: 17 - Sayı: 1

Isolated acquired FX deficiency: A case report

Sayfa
29–32
DOI
—

Özet

A female with no previous history of bleeding presented with active bleeding from multiple body sites, declining hemoglolobin levels, and markedly prolonged prothrombin times (PT), and activated par-tial thromboplastin times (APTT) with incomplete correction on PT mix assays. This patient showed a severe deficiency of factor X. FX levels and bleeding were refractory to multiple transfusions of fresh fro-zen plasma. Although plasmapheresis was started with concomitant intravenous immunoglobulin and steroid therapy, the patient died.

Anahtar kelimeler: Steroidler,Kan pıhtılaşma bozuklukları, kalıtsal,Erişkin,Faktör X eksikliği,Protrombin zamanı,Ölümle sonuçlanma