Dergiler / Turkish Journal of Rheumatology(.)Archives of Rheumatology / 2013 / Cilt: 28 - Sayı: 3
Dermatomyositis Associated with Laryngeal Rhabdomyosarcoma: A Case Report
- Sayfa
- 202–205
- DOI
- —
Özet
Dermatomyosit kütanöz bulgularla karakterize olan sistemik, otoimmün, inflamatuvar ve çeşitli malignite tipleri ile ilişkili bir hastalıktır. Rabdomyosarkom, rabdomyoblast olarak adlandırılan primitif kas hücrelerinden köken alan ve hızlı büyüyen malign mezenkimal bir neoplazidir. Rabdomyosarkom en sık baş ve boyun bölgesinde görülmektedir. Bilgimiz dahilinde dermatomyozit ve larengeal rabdomyosarkom birlikteliğine literatürde rastlanmamıştır. Bu makalede, cerrahi ve kemoradyoterapi ile tedavi edilen dermatomyozit ve larengeal rabdomyosarkom birlikteliği olan bir olgu sunuldu
Abstract
Dermatomyositis is a systemic autoimmune inflammatory disorder which is characterized by cutaneous manifestations and associated with various types of malignancies. Rhabdomyosarcoma is a rapidly growing, malignant mesenchymal neoplasm which arises from primitive muscle cells known as rhabdomyoblasts. The head and neck are the primary sites for rhabdomyosarcoma. To the best of our knowledge, concurrent dermatomyositis and rhabdomyosarcoma have not been reported before. In this article, we present a case with dermatomyositis and laryngeal rhabdomyosarcoma who was treated with surgery and chemoradiotherapy