Intravascular leiomyoma with intracardiac extension associated with hepatorenal polycystic disease

Özet

We present the case of a woman with hepato-renal polycysticdisease and chronic hemodialysis admitted for paroxysmal atrialfibrillation. A right heart mass was diagnosed by echocardiography. MRI and angio-CT scans confirmed a calcified tumor withthe origin in the right internal iliac vein that extended through inferior vena cava to the right cardiac chambers. The intracardiactumor was excised by cardiovascular surgery due to perceivedpulmonary embolic risk. The tumor mass was a leyomyoma. Despite extensive inferior vena cava extension, tumor dimensionsdid not increase at one year follow-up and no intracardiac recurrence was noticed.