DİSTROFİK EPİDERMOLİZİS BÜLLOZADA LAPAROSKOPİK APENDEKTOMİ: MİNİMAL İNVAZİV GİRİŞİMİN AVANTAJLARI

LAPAROSCOPIC APPENDECTOMY IN DYSTROPHIC EPIDERMOLYSIS BULLOSA: ADVANTAGES OF MINIMALLY INVASIVE PROCEDURE

Çiğdem ARSLAN ALICI,M. Surhan ARDA,HÜSEYİN İLHAN,AYDAN AYŞE KÖSE,BARAN TOKAR

Özet

Distrosfik epidermolizis bülloza (DEB), bül oluşumunun

Abstract

Dystrophic epidermolysis bullosa (DEB) is anepidermolysis bullosa (EB) type that bulla formationdevelops on the dermal surface of thedermoepidermal component due to splitting inthe basal lamina. In these patients, opening ofmechanical blisters caused by trauma can leadto infection.In cases with DEB, surgical intervention, especiallyin the case of abdominal surgery, requirescareful attention to prevent infection of theblisters caused by incision and surgery. Here wepresent a 16-year-old male having DEB who hadundergone laparoscopic appendectomy with adiagnosis of perforated appendicitis. Preoperativeand postoperative interventions have to beplanned to cause minimal trauma and infectionto the skin and preference for a less invasive laparoscopicapproach is the approach

Anahtar kelimeler: Epidermolizis bülloza, Distrosfik epidermolizis bülloza, Perfore apendisit, Laparoskopik appendektomi