Dergiler / Erciyes Medical Journal / 2018 / Cilt: 40 - Sayı: 2

Chronic Granulomatous Disease in a Boy Who Presented With Dactilitis Caused by Serratia Marcescens, Mimicking Rheumatic Monoarthritis in the Newborn Period: A Case Presentation

Sayfa
95–98
DOI
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Özet

Chronic granulomatous disease (CGD) is a heterogenous genetic primary immune deficiency disorder, characterized by lifethreatening infections and granulomas secondary to increased inflammatory responses. Most infections involve the lungs, skin, lymph nodes, and liver. Wedescribe a child diagnosed with CGD and the p67phox mutation presenting with Serratia marcescens arthritis without osteomyelitis in the newborn period.

Chronic Granulomatous Disease in a Boy Who Presented With Dactilitis Caused by Serratia Marcescens, Mimicking Rheumatic Monoarthritis in the Newborn Period: A Case Presentation — AJIndex