Dergiler / Çocuk Dergisi / 2026 / Cilt: 23 Sayı: 2

Successful Repair of Congenital Morgagni Hernia and Ventricular Septal Defect via Median Sternotomy in a Patient with Down Syndrome, Anal Atresia, Pectus Carinatum and Congenital Hypothyroidism

Buğra Harmandar(Muğla Sıtkı Koçman University Medical Faculty, Department of Cardiovascular Surgery)0000-0002-7487-1779
Hande İştar(Muğla Sıtkı Koçman University Medical Faculty, Department of Cardiovascular Surgery)0000-0002-7150-0171
Sayfa
195–197
Yayın Tarihi
2023-06-30
🏛️Bu makalenin bibliyografik verileri ve tam metin bağlantısı DergiPark üzerinden sağlanmıştır.
DergiPark Kaydı ↗
✨

Yapay Zeka Hızlı Bakış & Çıkarımlar

AI Insight
⚡ TL;DR(1 Cümlede Hızlı Çıkarım)

Postoperatif seyir sorunsuzdu.

📌 3 Maddede Bu Makale

🎯
Amaç & Hipotez:Olgu sunumumuzda, 5 aylık Down sendromlu kız hastada yapılan başarılı konjenital Morgagni hernisi ve ventrikül septal defekt onarımını sunmaktayız.
📊
Temel Bulgular & Veri:Median sternotomi yaklaşımıyla aynı seansta yapılan onarımlarda kardiyopulmoner bypass eşliğinde VSD, polytetrafluoroethylene yama ile kapatıldı.
💡
Sonuç & Katkı:Postoperatif seyir sorunsuzdu.
🔬Tür:Araştırma Makalesi
📍Kapsam:Genişletilmiş Akademik Örneklem
⚙️Değişkenler:Morgagni Hernisi · Hipotiroidi · Ventriküler Septal Defekt

Özet

Olgu sunumumuzda, 5 aylık Down sendromlu kız hastada yapılan başarılı konjenital Morgagni hernisi ve ventrikül septal defekt onarımını sunmaktayız. Median sternotomi yaklaşımıyla aynı seansta yapılan onarımlarda kardiyopulmoner bypass eşliğinde VSD, polytetrafluoroethylene yama ile kapatıldı. Diaframdaki defekt ise primer olarak, transabdominal yaklaşıma gerek olmadan onarıldı. Postoperatif seyir sorunsuzdu.

Abstract

Here we report a 5-month-old female patient with Down syndrome who was successfully operated on due to congenital Morgagni hernia and ventricular septal defect concomitantly via median sternotomy. Ventricular septal defect was repaired with a polytetrafluoroethylene patch through the right atriotomy using cardiopulmonary bypass, and diaphragmatic hernia was repaired primarily with prolene sutures reinforced with teflon pledgets after excising the diaphragmatic hernia pouch simultaneously. Entire operation was completed via median sternotomy, and transabdominal approach was not required to repair the diaphragmatic hernia. Postoperative course was uneventful.

🔖

Bu Makaleye Atıf Yap

Harmandar, B., İştar, H. (2023). Successful Repair of Congenital Morgagni Hernia and Ventricular Septal Defect via Median Sternotomy in a Patient with Down Syndrome, Anal Atresia, Pectus Carinatum and Congenital Hypothyroidism. Çocuk Dergisi, Cilt: 23 Sayı: 2, 195–197. https://doi.org/10.26650/jchild.2023.1091955

📄 Tam Metin PDF Okuyucu

📄

PDF görüntüleyici hazırlanıyor...

Kaynakça (13)

  1. Bassareo PP, Neroni P, Montis S, Tumbarello R. Morgagni’s diaphragmatic hernia mimicking a severe congenital heart disease in a newborn: a case report. J Med Case Rep 2010; 4: 395. google scholar
  2. Yang W, Carmichael SL, Harris JA, Shaw GM. Epidemiologic characteristics of congenital diaphragmatic hernia among 2.5 million California births, 1989-1997. Birth Defects Res A Clin Mol Teratol 2006; 76: 170-4. google scholar
  3. deHoyos A. Foramen of morgagni hernia. In: Shields TW, LoCicero JR, Reed CE, editors. General thoracic surgery. 7th ed. Philadelphia: Lippincott Williams & Wilkins; 2009. p. 719-24. google scholar
  4. Al-Salem AH. Congenital hernia of Morgagni in infants and children. J Pediatr Surg 2007; 42: 1539-43. google scholar
  5. Adebo OA, MB, BS, FRCS(C), DABS, DABTS et all. Scimitar Syndrome with associated Morgagni hernia in a Nigerian infant. J Nati Med Assoc 1979; 71: 10. google scholar
  6. Pokorny WJ, McGill CW, Harberg FJ. Morgagni hernias during infancy: Presentation and associated anomalies. J Pediatr Surg 1984; 19: 394-7. google scholar
  7. Deng X, Liu P, Yi L, Wang J, Huang P. A rare case of Morgagni hernia associated with cor triatriatum. J Pediatr Surg Case Rep 2015; 3: 19-21. google scholar
  8. Berman L, Stringer D, Ein SH, Shandling B. The late-presenting pediatric morgagni hernia: A benign condition. J Pediatr Surg 1989; 24: 970-2. google scholar
  9. Rashid F, Chaparala R, Ahmed J, Iftikhar SY. Atypical right diaphragmatic hernia (hernia of Morgagni), spigelian hernia and epigastric hernia in a patient with Williams syndrome: a case report. J Med Case Rep 2009; 3: 7. google scholar
  10. Mert M, Gunay I. Transsternal repair of Morgagni hernia in a patient with coexistent ventricular septal defect and Down syndrome. Acta Chirurgica Belgica 2006; 106: 739-40. google scholar
  11. Oppelt PU, Askevold I, Bender F, Liese. J, Padberg W, Hecker A et al. Morgagni-Larrey diaphragmatic hernia repair in adult patients: a retrospective single-center experience. Hernia 2021 25: 479-89. google scholar
  12. Daifoladi A A, Talemi H G, Rezaei M A, Wardak A F, Negin F, Mousavi S H. Concomitant trans-sternal repair of Morgagni hernia and ventricular septal defect in a patient with Down syndrome: A case report. Int J Surg Case Rep 2022; 92: 106911. google scholar
  13. Shahri H M M, Ghiasi S S, Shaye Z A, Zegheibizadeh F. Congenıtal heart defects in infants with a congenital diaphragmatic hernia: a single-center experience. Pak Heart J. 2022;55(04): 408-12. google scholar