The aim of this study is to investigate factors associated with severe lung disease in a cohort of adult patientswith CF.Materials and methods: Demographic data, clinical and laboratory findings of the patients aged 18 years and more were collected andthe patients were grouped according to forced expiratory volume in 1 s (FEV1) as severe group:
📌 3 Maddede Bu Makale
🎯
Amaç & Hipotez:Background/Aim: The patients with cystic fibrosis (CF) are living longer compared to the past, but respiratory failure is still the mostcommon cause of mortality.
📊
Temel Bulgular & Veri:Background/Aim: The patients with cystic fibrosis (CF) are living longer compared to the past, but respiratory failure is still the mostcommon cause of mortality.
💡
Sonuç & Katkı:The aim of this study is to investigate factors associated with severe lung disease in a cohort of adult patientswith CF.Materials and methods: Demographic data, clinical and laboratory findings of the patients aged 18 years and more were collected andthe patients were grouped according to forced expiratory volume in 1 s (FEV1) as severe group:
🔬Tür:Araştırma Makalesi
📍Kapsam:Genişletilmiş Akademik Örneklem
⚙️Değişkenler:Alan Parametreleri
Abstract
Background/Aim: The patients with cystic fibrosis (CF) are living longer compared to the past, but respiratory failure is still the mostcommon cause of mortality. The aim of this study is to investigate factors associated with severe lung disease in a cohort of adult patientswith CF.Materials and methods: Demographic data, clinical and laboratory findings of the patients aged 18 years and more were collected andthe patients were grouped according to forced expiratory volume in 1 s (FEV1) as severe group:
🔖
Bu Makaleye Atıf Yap
DOĞRU, D., EMRİ, S., ER, B., ÇELEBİOĞLU, E., YALÇIN, E., ÖZÇELİK, U., KİPER, N., AKI, Ö. E., UZUN, Ö., AKOVA, M. (2022). Factors associated with severe lung disease in an adult population with cystic fibrosis: a single-center experience. Turkish Journal of Medical Sciences, Cilt: 50 - Sayı: 4, 945–952. https://ajindex.com/articles/609663
Annual Data Report. Bethesda, Maryland, USA: Cystic Fibrosis Foundation; 2017. 3. European Cystic Fibrosis Society Patient Registry. Annual Report 2016.
Karup, Denmark: European Cystic Fibrosis Society; 2018. 4. Plant BJ, Goss CH, Plant WD, Bell SC. Management of comorbidities in older patients with cystic fibrosis. Lancet Respiratory Medicine 2013; 1(2): 164-174. doi: 10.1016/S2213- 2600(13)70025-0 5. Zolin A, Bossi A, Cirilli N, Kashirskaya N, Padoan R. Cystic fibrosis mortality in childhood. Data from European Cystic Fibrosis Society Patient Registry. International Journal of Environmental Research and Public Health 2018; 15(9): 2020. doi: 10.3390/ijerph15092020 6. Kolodziej M, de Veer MJ, Cholewa M, Egan GF, Thompson BR. Lung function imaging methods in Cystic Fibrosis pulmonary disease. Respiratory Research 2017; 18(1): 96. doi: 10.1186/ s12931-017-0578-x 7. Dogru D, Cakir E, Sismanlar T, Cobanoglu N, Pekcan S et al. Cystic fibrosis in Turkey: First data from the national registry. Pediatric Pulmonology 2019; 55(2): 541-548. doi: 10.1002/ ppul.24561 8. Terheggen-Lagro S, Truijens N, van Poppel N, Gulmans V, van der Laag J et al. Correlation of six different cystic fibrosis chest radiograph scoring systems with clinical parameters. Pediatric Pulmonology 2003; 35(6): 441-445. doi: 10.1002/ppul.10280 9. Lee TW, Brownlee KG, Conway SP, Denton M, Littlewood JM. Evaluation of a new definition for chronic Pseudomonas aeruginosa infection in cystic fibrosis patients. Journal of Cystic Fibrosis 2003; 2(1): 29-34. doi: 10.1016/S1569-1993(02)00141- 8 10. Orenstein DM, Boat TF, Stern RC, Tucker AS, Charnock EL et al. The effect of early diagnosis and treatment in cystic fibrosis: a seven-year study of 16 sibling pairs. American Journal of Diseases of Children 1977; 131(9): 973-975. doi: 10.1001/ archpedi.1977.02120220039005 11. Southern KW, Munck A, Pollitt R, Travert G, Zanolla L et al. A survey of newborn screening for cystic fibrosis in Europe. Journal of Cystic Fibrosis 2007; 6(1): 57-65. doi: 10.1016/j. jcf.2006.05.008 12. Taylor-Robinson D, Whitehead M, Diderichsen F, Olesen HV, Pressler T et al. Understanding the natural progression in %FEV1 decline in patients with cystic fibrosis: a longitudinal study. Thorax 2012; 67(10): 860-866. doi: 10.1136/ thoraxjnl-2011-200953 13. Vandenbranden S