Dergiler / Trends in pediatrics / 2021 / Cilt: 2 - Sayı: 2

Langerhans Cell Histiocytosis with Isolated Central Diabetes Insipidus, Low Grade Fever and Sellar Erosion

Sayfa
104–108
Yayın Tarihi
2022-10-19
DOI
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⚡ TL;DR(1 Cümlede Hızlı Çıkarım)

The presence of low-grade fever in a patient presenting with isolated CDI is a warning sign for the diagnosis of LCH.

📌 3 Maddede Bu Makale

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Amaç & Hipotez:Langerhans cell histiocytosis (LCH) is a rare disease of the monocyte-macrophage system.
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Temel Bulgular & Veri:A 4-year-old, 5-month-old male patient who applied to our outpatient clinic was diagnosed with Langerhans cell histiocytosis in further examination after the diagnosis of central diabetes insipidus (CDI) was made.
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Sonuç & Katkı:The presence of low-grade fever in a patient presenting with isolated CDI is a warning sign for the diagnosis of LCH.
🔬Tür:Araştırma Makalesi
📍Kapsam:Genişletilmiş Akademik Örneklem
⚙️Değişkenler:Alan Parametreleri

Abstract

Langerhans cell histiocytosis (LCH) is a rare disease of the monocyte-macrophage system. Although it is known that bone involvement is seen very frequently in cases with LCH, our case is the first case with a lytic-destructive lesion in the bone structure forming sella turcica. A 4-year-old, 5-month-old male patient who applied to our outpatient clinic was diagnosed with Langerhans cell histiocytosis in further examination after the diagnosis of central diabetes insipidus (CDI) was made. On cranial magnetic resonance imaging (MRI), widespread lytic-destructive bone lesions were observed in the bone structure forming the sella (sphenoid bone), sellar destruction not previously described in the literature. Sellar erosion has not been reported before in cases diagnosed with LCH in the literature. The presence of low-grade fever in a patient presenting with isolated CDI is a warning sign for the diagnosis of LCH.

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Bu Makaleye Atıf Yap

Derinkuyu, B. E., Erdeve, Ş. S., Çetinkaya, S., Okur, İ., Arı, H., Çağlar, G., Çınar, H. G., Yeşil, Ş. (2022). Langerhans Cell Histiocytosis with Isolated Central Diabetes Insipidus, Low Grade Fever and Sellar Erosion. Trends in pediatrics, Cilt: 2 - Sayı: 2, 104–108. https://ajindex.com/articles/598908

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Kaynakça (9)

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