Dergiler / Trends in pediatrics / 2021 / Cilt: 2 - Sayı: 4

Phenylalanine Levels of Patients with Classical Phenylketonuria According to Eating Habits of Caregivers

Sayfa
154–158
Yayın Tarihi
2022-10-19
DOI
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⚡ TL;DR(1 Cümlede Hızlı Çıkarım)

Large-scale studies are needed to investigate the physical, social and psychological effects of parents’ dietary habits on PKU patients.

📌 3 Maddede Bu Makale

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Amaç & Hipotez:Objective: Diet is the main component in the treatment of classical phenylketonuria (PKU).
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Temel Bulgular & Veri:Methods: The parents of 32 PKU patients were asked about their socio-demographic characteristics, family dietary patterns (mealtimes; frequency of meals with the PKU patient; content of foods at mealtimes, etc.) the parental dietary regimen and any food allergies.
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Sonuç & Katkı:Large-scale studies are needed to investigate the physical, social and psychological effects of parents’ dietary habits on PKU patients.
🔬Tür:Araştırma Makalesi
📍Kapsam:Genişletilmiş Akademik Örneklem
⚙️Değişkenler:Alan Parametreleri

Abstract

Objective: Diet is the main component in the treatment of classical phenylketonuria (PKU). Living in the same house as a PKU patient affects the lifestyle of family members in many ways. The present study examines the dietary habits of the parents of PKU patients. Methods: The parents of 32 PKU patients were asked about their socio-demographic characteristics, family dietary patterns (mealtimes; frequency of meals with the PKU patient; content of foods at mealtimes, etc.) the parental dietary regimen and any food allergies. Results: The mean age of the PKU patients was 11.5±4.3 years, and 14 (44%) were female. The mean plasma phenylalanine (Phe) level over the previous year was 732.4±339.0 μmol/L in the patient group. Within the study sample, 2 (6%) families prepared only low-protein meals in the home, and the Phe levels of the two PKU patients in these families never exceeded >600 μmol/L, and 26 (81%) parents prepared separate meals for the PKU patient and for the other family members every day. The 28 (88%) parents had no special dietary regimen, with a mean Phe level of 774.8±345.4 μmol/L (p=0.055). Finally, 26 (81%) of the parents were careful about the foods they consumed while eating with the PKU patient, opting especially for foods that are low in Phe. Conclusion: Diet is an indispensable part of the treatment of PKU and can affect the dietary patterns also of parents. Phe levels are lower in the children of parents who adopt a protein-restricted diet as a lifestyle, such as vegan and pescetarian. Large-scale studies are needed to investigate the physical, social and psychological effects of parents’ dietary habits on PKU patients.

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Bu Makaleye Atıf Yap

ARSLAN, N., GÜNEŞ, A., KARAGÖZ, H., YAVAŞ, G., DAĞ, M., KISA, P. T. (2022). Phenylalanine Levels of Patients with Classical Phenylketonuria According to Eating Habits of Caregivers. Trends in pediatrics, Cilt: 2 - Sayı: 4, 154–158. https://ajindex.com/articles/598903

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Kaynakça (13)

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