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Dergiler / İstanbul Kuzey Klinikleri / 2021 / Cilt: 8 - Sayı: 6

Giant composite pheochromocytoma and gastrointestinal stromal tumor in a patient with neurofibromatosis: A case report

Ali Emre NAYCI
Soykan ARIKAN
Cihad TATAR
Feyzullah ERSOZ
Mehmet Baki DOĞAN
Feray GÜNER
Sayfa
629–633
Yayın Tarihi
2022-10-18
DOI
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Yapay Zeka Hızlı Bakış & Çıkarımlar

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⚡ TL;DR(1 Cümlede Hızlı Çıkarım)

Therefore, we aimed to present this rare case with a literature background.

📌 3 Maddede Bu Makale

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Amaç & Hipotez:A 54-year-old male was admitted to our department with neurofibromatosis and hypertension.
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Temel Bulgular & Veri:A mass with 30×23 cm in size was removed.
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Sonuç & Katkı:Therefore, we aimed to present this rare case with a literature background.
🔬Tür:Araştırma Makalesi
📍Kapsam:Genişletilmiş Akademik Örneklem
⚙️Değişkenler:Alan Parametreleri

Abstract

A 54-year-old male was admitted to our department with neurofibromatosis and hypertension. During his examination, a mass was detected in the abdomen, and he was transferred to a surgical clinic. At the first examination of the patient, extensive café-au-lait spots and granulomas were detected on the body and the mass occupying right abdomen quadrant was palpable. The patient’s medical history indicated that he had hypertension for almost a decade. The patient also stated that nodules on the body existed from his earliest recollection and he had relatives with neurofibromatosis. The patient was taken to a surgical operation. A mass with 30×23 cm in size was removed. The area of the nodular structure, with 0.5 cm in diameter, in the stomach serosa was also removed. The tumor was composed of phaeochromocytoma in the larger spaces and ganglioneuromas in the relatively narrow spaces. The nodular area removed in gastric serosa was reported as a very low-risk gastrointestinal stromal tumor. Apart from this rare combination, adrenal mass removed from the patient was considerably larger than the masses in the literature until now. Therefore, we aimed to present this rare case with a literature background.

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Bu Makaleye Atıf Yap

NAYCI, A. E., ARIKAN, S., TATAR, C., ERSOZ, F., DOĞAN, M. B., GÜNER, F. (2022). Giant composite pheochromocytoma and gastrointestinal stromal tumor in a patient with neurofibromatosis: A case report. İstanbul Kuzey Klinikleri, Cilt: 8 - Sayı: 6, 629–633. https://ajindex.com/articles/551242

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Kaynakça (14)

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