Dergiler / Turkish Journal of Anaesthesiology and Reanimation / 2022 / Cilt: 50 - Sayı: 1

Anaesthetic Management of a Child with West Syndrome Associated with Tuberous Sclerosis Complex at a Remote Location: A Case Report

Sayfa
72–74
DOI
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⚡ TL;DR(1 Cümlede Hızlı Çıkarım)

Thorough knowledge of the disease process, its manifestation and its management is the key to the successful management of such cases.

📌 3 Maddede Bu Makale

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Amaç & Hipotez:West syndrome is a rare syndrome that consists of a triad of infantile spasms, hypsarrhythmia pattern on electroencephalogram and mental retardation.
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Temel Bulgular & Veri:Tuberous sclerosis complex (TSC) is one of the disorders that can cause it.
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Sonuç & Katkı:Thorough knowledge of the disease process, its manifestation and its management is the key to the successful management of such cases.
🔬Tür:Araştırma Makalesi
📍Kapsam:Genişletilmiş Akademik Örneklem
⚙️Değişkenler:Alan Parametreleri

Özet

West syndrome is a rare syndrome that consists of a triad of infantile spasms, hypsarrhythmia pattern on electroencephalogram and mental retardation. Tuberous sclerosis complex (TSC) is one of the disorders that can cause it. Radiology suites are considered as remote locations for anaesthesiologists, and the delivery of anaesthesia becomes challenging if a patient with such a rare disease having multiple anaesthetic implications arrives. We present anaesthetic management for the radiological procedure of the MRI brain of a year old paediatric patient with the West syndrome having suspected TSC based on presenting signs and symptoms. Anaesthetic consideration and management of this rare syndrome are discussed. Detailed preoperative assessment, pre-emptive preparation for possible difficult intubation and difficult intravenous access, careful positioning and prevention of seizures should be the goal. Thorough knowledge of the disease process, its manifestation and its management is the key to the successful management of such cases.

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Bu Makaleye Atıf Yap

HAMEED, M., HAQ, M. I. U. (2022). Anaesthetic Management of a Child with West Syndrome Associated with Tuberous Sclerosis Complex at a Remote Location: A Case Report. Turkish Journal of Anaesthesiology and Reanimation, Cilt: 50 - Sayı: 1, 72–74. https://ajindex.com/articles/418178

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