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Dergiler / Turkish Journal of Hematology / 2001 / Cilt: 18 - Sayı: 3

Homozygous Beta-Thalassemia associated with Familial Mediterranean Fever in a Turkish patient

Duran CANATAN
Rüya COŞAN
HAKKI TAŞTAN
Onur BİLENOĞLU
A. Nazlı BAŞAK
Sayfa
195–197
DOI
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⚡ TL;DR(1 Cümlede Hızlı Çıkarım)

Our patient's clinical course revealed a possible synergistic effect between colchicine and desferrioxamine (DFO) However, this could be a only a coincidence, as under colchicine therapy, fever attacks may appear, this may be the topic of a further investigation.

📌 3 Maddede Bu Makale

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Amaç & Hipotez:We report here a ß- thalassemia major case (homozygous IVS-1-110 G-A) associated with Familial Mediterranean Fever (FMF) (homozygous 694 Met-Val).
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Temel Bulgular & Veri:We report here a ß- thalassemia major case (homozygous IVS-1-110 G-A) associated with Familial Mediterranean Fever (FMF) (homozygous 694 Met-Val).
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Sonuç & Katkı:Our patient's clinical course revealed a possible synergistic effect between colchicine and desferrioxamine (DFO) However, this could be a only a coincidence, as under colchicine therapy, fever attacks may appear, this may be the topic of a further investigation.
🔬Tür:Araştırma Makalesi
📍Kapsam:Genişletilmiş Akademik Örneklem
⚙️Değişkenler:Kolşisin · Ailesel akdeniz ateşi · beta-Talasemi

Özet

We report here a ß- thalassemia major case (homozygous IVS-1-110 G-A) associated with Familial Mediterranean Fever (FMF) (homozygous 694 Met-Val). Our patient's clinical course revealed a possible synergistic effect between colchicine and desferrioxamine (DFO) However, this could be a only a coincidence, as under colchicine therapy, fever attacks may appear, this may be the topic of a further investigation.

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Bu Makaleye Atıf Yap

CANATAN, D., COŞAN, R., TAŞTAN, H., BİLENOĞLU, O., BAŞAK, A. N. (2001). Homozygous Beta-Thalassemia associated with Familial Mediterranean Fever in a Turkish patient. Turkish Journal of Hematology, Cilt: 18 - Sayı: 3, 195–197. https://ajindex.com/articles/413061

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Kaynakça (9)

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