In this case presentation, a 13-year-oldadolescent with Gaucher disease on enzyme replacement treatment was presented, who was detected having an abdominal mass on a routine visit and diagnosed with partial torsion of a wandering spleen associated with left lobe hypoplasia of the liver
📌 3 Maddede Bu Makale
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Amaç & Hipotez:A wandering spleen is a rare condition characterized by the malposition of the spleen due to laxity or absence of its supporting ligaments.
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Temel Bulgular & Veri:Although Gaucher disease generally presents with massive splenomegaly, which one of the predisposing causes of a wandering spleen, literature shows only one report of a wandering spleen in a child with Gaucher disease.
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Sonuç & Katkı:In this case presentation, a 13-year-oldadolescent with Gaucher disease on enzyme replacement treatment was presented, who was detected having an abdominal mass on a routine visit and diagnosed with partial torsion of a wandering spleen associated with left lobe hypoplasia of the liver
🔬Tür:Araştırma Makalesi
📍Kapsam:Genişletilmiş Akademik Örneklem
⚙️Değişkenler:Alan Parametreleri
Özet
A wandering spleen is a rare condition characterized by the malposition of the spleen due to laxity or absence of its supporting ligaments. Although Gaucher disease generally presents with massive splenomegaly, which one of the predisposing causes of a wandering spleen, literature shows only one report of a wandering spleen in a child with Gaucher disease. In this case presentation, a 13-year-oldadolescent with Gaucher disease on enzyme replacement treatment was presented, who was detected having an abdominal mass on a routine visit and diagnosed with partial torsion of a wandering spleen associated with left lobe hypoplasia of the liver
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Bu Makaleye Atıf Yap
GÜNGÖR, Ş., ÖZTÜRK, M., VAROL, F. İ., SIĞIRCI, A., SELİMOĞLU, M. A. (2017). Torsion of a wandering spleen in an adolescent with Gaucher disease. Turkish Journal of Gastroenterology, Cilt: 28 - Sayı: 4, 303–306. https://ajindex.com/articles/411074
Baykara M, Karahan OI, Coşkun A. Case report: Acute abdomen and pelvic mass due to of wandering spleen. Diagn Interv Radiol 2003; 9: 105-7
Misawa T, Yoshida K, Shiba H, Kobayashi S, Yanaga K. Wandering spleen with chronic torsion. Am J Surg 2008; 195: 504-5
Brown CV, Virgilio GR, Vazquez WD. Wandering spleen and its complications in children: a case series and review of the literature. J Pediatr Surg 2003; 38: 1676-9
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Vinnakota S, Jayasree N. New insight into the morphology of the human liver: a cadaveric study. ISRN Anat 2013; 2013: 689564
Kakitsubata Y, Nakamura R, Mitsuo H, Suzuki Y, Kakitsubata S, Watanabe K. Absence of the left lobe of the liver: US and CT appearance. Gastrointest Radiol 1991; 16: 323-5.