However, an upfront emergency radical nephrectomy should be discussed.
📌 3 Maddede Bu Makale
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Amaç & Hipotez:We report a rare case of a spontaneous Wilms tumor rupture in a 13-month-old male who presented with a rapidly increasing abdominal distension.
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Temel Bulgular & Veri:The child had acute exacerbation of symptoms which precipitated an emergency left radical nephrectomy and renal venectomy (due to densely adherent tumoral embolus in left renal vein and Inferior Vena Cava) indicated for intraperitoneal tumor rupture.
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Sonuç & Katkı:However, an upfront emergency radical nephrectomy should be discussed.
🔬Tür:Araştırma Makalesi
📍Kapsam:Genişletilmiş Akademik Örneklem
⚙️Değişkenler:Alan Parametreleri
Özet
We report a rare case of a spontaneous Wilms tumor rupture in a 13-month-old male who presented with a rapidly increasing abdominal distension. The child had acute exacerbation of symptoms which precipitated an emergency left radical nephrectomy and renal venectomy (due to densely adherent tumoral embolus in left renal vein and Inferior Vena Cava) indicated for intraperitoneal tumor rupture. Postoperative histopathology confirmed a Wilms tumor; classified as stage IIIc. He is on a three-drug chemotherapy and doing well on follow-up. Preoperative spontaneous Wilms tumor rupture is a clinico-radiological challenge. A high index of suspicion is a prerequisite for diagnosis. However, an upfront emergency radical nephrectomy should be discussed.
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Bu Makaleye Atıf Yap
GUPTA, R., MATHUR, P., SHARMA, G., PARİHAR, P. S., MİTTAL, P. (2021). Spontaneous Wilms Tumor Rupture: A Preoperative Clinical Diagnosis. Üroonkoloji Bülteni, Cilt: 20 - Sayı: 4, 276–279. https://ajindex.com/articles/401898
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