Lokal rekürens bulunmaksızın akciğer metastazı gösteren dermatofibrosarkom protüberans

Abstract

Dermatofibrosarcoma protuberans is a rare skin tumor which constitutes 6% of soft tissue sarcomas. Typically, it has a superficial location and a locally aggressive character. Although it has a relatively high recurrence rate, the rate of distant metastasis is about 3%. Furthermore, it rarely metastasizes without local recurrence. Here we present a case with dermatofibrosarcoma protuberans with distant metastasis occurring seven years after the local excision of the primary tumor and without any local recurrence.