Dergiler / PTT Hastanesi Tıp Dergisi / 2002 / Cilt: 24 - Sayı: 3

Agamaglobüllinemi ile seyreden "Common Variable Immunodeficiency Disease"

Common variable immunodeficiency accompanted by agammaglobulinemia: A case report

Sayfa
155–157
DOI
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⚡ TL;DR(1 Cümlede Hızlı Çıkarım)

Ay-lık 200 mg insan gamaglobülin replasmanı planlanarak takibe alındı.

📌 3 Maddede Bu Makale

🎯
Amaç & Hipotez:"Common variable immunodeficiency disease" primer gamaglobulin düşüklüğüyle seyreden, yaygın bir hasta-lıktır.
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Temel Bulgular & Veri:B hücrelerinin varlığıyla X'e bağlı agamaglobüli-nemiden (Bruton agamaglobülinemi) ayrılır.
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Sonuç & Katkı:Ay-lık 200 mg insan gamaglobülin replasmanı planlanarak takibe alındı.
🔬Tür:Araştırma Makalesi
📍Kapsam:Genişletilmiş Akademik Örneklem
⚙️Değişkenler:İmmün yetmezlik sendromları · Agamaglobulinemi · Tanı

Özet

"Common variable immunodeficiency disease" primer gamaglobulin düşüklüğüyle seyreden, yaygın bir hasta-lıktır. B hücrelerinin varlığıyla X'e bağlı agamaglobüli-nemiden (Bruton agamaglobülinemi) ayrılır. Otuz yaşın-daki kadın hasta ateş, öksürük, balgam çıkarma ve sağ yan ağrısı şikayetleri ile başvurdu. Öyküsünde tekrarla-yan üst ve alt solunum yolları hastalığı ve lober pnömo-ni tablosu vardı. İncelemeler sonucunda "common vari-able immunodeficiency disease" tanısı kondu. Normal-de bu hastalık gamaglobülin düşüklüğü ile seyrederken hastamızda agamaglobülinemi vardı. Hasta uygun anti-biyotiklerle ve insan gamaglobülini ile tedavi edildi. Ay-lık 200 mg insan gamaglobülin replasmanı planlanarak takibe alındı.

Abstract

Common variable immunodeficiency (CVID) is a common primary immunodeficiency disease characterized by hypogammaglobulinemia. It differs from X-linked agamma-globulinemia (Bruton's agammaglobulinemia) by the pres-ence of B cells. A-thirty-year-old woman presented with fever, cough, expectoration of sputum, and pain on her right side. She had a history of recurrent upper and lower respi-ratory tract disease and lobar pneumonia. Examinations enabled to draw a diagnosis of common variable immunod-eficiency disease. Although this disease is accompanied by low levels of gammaglobulin, the patient had agammaglob-ulinemia. She was treated with antibiotics and human gam-maglobulin. She was included in a follow-up program with a monthly administration of 200 mg human gammaglobulin.

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Bu Makaleye Atıf Yap

UYANIKOĞLU, A., BENZER, M., GÜNEY, M. (2002). Agamaglobüllinemi ile seyreden "Common Variable Immunodeficiency Disease". PTT Hastanesi Tıp Dergisi, Cilt: 24 - Sayı: 3, 155–157. https://ajindex.com/articles/340416

Kaynakça (8)

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