Noonan sendromlu bir olguda triküspit atrezisi

Amaç & Hipotez:Noonan sendromunda %50-80 oranında kalp hastalıkları görülürken, en sık saptanan kardiyak anomaliler pulmoner stenoz ve hipertrofik kardiyomiyopatidir.

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Temel Bulgular & Veri:Noonan sendromunda %50-80 oranında kalp hastalıkları görülürken, en sık saptanan kardiyak anomaliler pulmoner stenoz ve hipertrofik kardiyomiyopatidir.

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Sonuç & Katkı:Noonan sendromu ile triküspid atrezisi literatürde hiç bildirilmemiş olması nedeniyle sunulmuştur.

🔬Tür:Literatür & Derleme Çalışması

📍Kapsam:Genişletilmiş Akademik Örneklem

⚙️Değişkenler:Triküspit atrezi · Noonan sendromu · Tricuspid Atresia

Özet

Noonan sendromunda %50-80 oranında kalp hastalıkları görülürken, en sık saptanan kardiyak anomaliler pulmoner stenoz ve hipertrofik kardiyomiyopatidir. Noonan sendromu ile triküspid atrezisi literatürde hiç bildirilmemiş olması nedeniyle sunulmuştur.

Abstract

The prevalence of congenital heart defect in Noonan syndrome varies from 50 to 80%, however pulmonary stenosis and hypertrophic cardiomyopathy are generally the most common congenital heart defects found in Noonan syndrome.

Anahtar kelimeler

Triküspit atrezi Noonan sendromu Tricuspid Atresia Noonan Syndrome

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Bu Makaleye Atıf Yap

ALPAN, N., ÇAKIR, H. T., ÇAKIR, B. Ç., SEL, K. (2004). Noonan sendromlu bir olguda triküspit atrezisi. Medical Network Klinik Bilimler ve Doktor, Cilt: 10 - Sayı: 4, 434–437. https://ajindex.com/articles/278468

Kaynakça (14)

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