Baş-boyun bölgesi fibröz displazileri

Amaç: Baş-boyun bölgesi fibröz displazilerine cerrahi yaklaşımlarımızı sunmak ve sonuçlarımızı değerlendirmek. Hastalar ve Yöntemler: Baş-boyun bölgesi fibröz displazili 8 olgu bu çalışma kapsamına alındı. Preoperatif dönemde bilgisayarlı tomografi ile değerlendirilerek lezyonun sınırları belirlendi. Olgular orijin aldıkları bölgelere göre farklı cerrahi tekniklerle opere edildiler. Postoperatif morbidite, komplikasyon, nüks ve malign transformasyon değerlendirildi. Bulgular: Olguların 3'ü kadın, 5'i erkek ve ortalama yaş 18.3 idi. Tümörler, temporal kemik (n=2), maksilla (n=2), frontal kemik (n=2) ve sfenoid kemik (n=2)'ten orijin almakta idi. Lezyon lokalizasyonuna göre, dış kulak yolunda darlık, iletim tipi işitme kaybı, başağrısı, yüzde deformite, burun tıkanıklığı ve maloklüzyon tesbit edilen semptomlardı. Fronto-orbital yaklaşım, Le-Fort I osteotomisi, modifiye radikal mastoidektomi ve parsiyal-inferior maksillektomi tümör orijinine göre uyguladığımız cerrahi tekniklerdi. Parsiyal-inferior maksillektomi uygulanan bir olguda oroantral fistül gelişti ve mukozal yanak flebi ile rekonstrükte edildi. 64.8 ay olan ortalama takip süresinde nüks ya da malign transformasyon izlenmedi. Sonuç: Fibröz displazi gelişimsel benign bir kemik tümörüdür. Cerrahi tedavi kararı patolojinin neden olduğu fonksiyonel ya da estetik bozukluğa göre verilir. Prognoz çoğunlukla iyidir. Ancak malign transformasyon da rapor edilmiştir. Bu nedenle uzun süreli hasta takibi gerekir.

Abstract

Objectives: To evaluate our surgical approaches and results to fibrous dysplasia in the head and neck area. Patients and Methods: Eight cases with head and neck fibrous dysplasia have been included in this study. In preoperative period the limits of the lesion has been determined with computed tomography. Cases have been operated with different techniques due to their origins. The postoperative morbidity, complications, recurrence and malignant transformation were evaluated. Results: Three of the cases were female and five cases were male. The average age was 18.3. The tumor was originated from temporal bone (n=2), maxillar bone (n=2), frontal bone (n=2) and sphenoid bone (n=2). External auditory canal stenosis, conductive hearing loss, headache, facial deformity, nasal airway obstruction, maloclusion were among the symptoms and fronto-orbital approach, Le-Fort-I osteotomy, partial-inferior maxillectomy, modified radical mastoidectomy were our surgical techniques performed according to the tumor localization. In one case which partial-inferior maxillectomy performed , oroantral fistula occured as a complication. It was reconstructed with mucosal cheek flap. In 64.8 months which was the average follow-up period recurrence or malignant transformation was not observe. Conclusion: Fibrous dysplasia is a developmental benign bone tumor. The surgical decision is made occourding to the functional or esthetic disorder it causes. Prognosis is usually good but malignant transformation can also be seen. Thus long-term follow-up is required.

Anahtar kelimeler

Üst çene Temporal kemik Kemiğin fibröz displazisi Frontal kemik Sfenoid kemik Maxilla Temporal Bone Fibrous Dysplasia of Bone Frontal Bone Sphenoid Bone

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Bu Makaleye Atıf Yap

ÜLKÜ, Ç. H., UYAR, Y., ARBAĞ, H., ACAR, O., ÖZTÜRK, K. (2002). Baş-boyun bölgesi fibröz displazileri. KBB-Forum, Cilt: 1 - Sayı: 3, 61–65. https://ajindex.com/articles/209431

Kaynakça (1)

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