H e r e , w e r e p o r t e d a n e w b o r n cas e di a g n o s e d w i th mo d e r a te h e m ophi l ia A , w i tho u t t he p re s en c e o f a p ositi v e f a mi l y hi s to r y of h e m ophi l ia an d p re s en t i n g w i th i n t r ac r a n i a l a n d e x t r ac r a n i a l h e m o rr h a g e a n d w e a i m e d to e mph as ize th a t the e a r l y dia g n osis an d r e p l ac e m e n t t h er a py ca rr i e s a n e ss e n tial im p o r t a n c e .
📌 3 Maddede Bu Makale
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Amaç & Hipotez:Normal 0 21 false false false TR X-NONE X-NONE /* Style Definitions */ table.MsoNormalTable {mso-style-name:"Normal Tablo"; mso-tstyle-rowband-size:0; mso-tstyle-colband-size:0; mso-style-noshow:yes; mso-style-priority:99; mso-style-qformat:yes; mso-style-parent:""; mso-padding-alt:0cm 5.4pt 0cm 5.4pt; mso-para-margin:0cm; mso-para-margin-bottom:.0001pt; mso-pagination:widow-orphan; font-size:11.0pt; font-family:"Calibri","sans-serif"; mso-ascii-font-family:Calibri; mso-ascii-theme-font:minor-latin; mso-fareast-font-family:"Times New Roman"; mso-fareast-theme-font:minor-fareast; mso-hansi-font-family:Calibri; mso-hansi-theme-font:minor-latin; mso-bidi-font-family:"Times New Roman"; mso-bidi-theme-font:minor-bidi;} In tr ac r a n i a l h e m o r r h a ge a mo n g t e r m n e w b o r n s is a r ar e cl i n i ca l c o n di t ion w i t h high m o rb i dity a n d m o r t al ity.
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Temel Bulgular & Veri:Al though m a jor b le e d i n g is re la tiv e l y u n c om m o n , t h e i nc id en c e of i n t r ac r a n i a l h e m o rr h a g e in h e m ophi l ic c hi l d r e n is hig h e r dur i n g t h e f i r s t f e w d a ys of l ife th a n a t a n y ot h e r s t a ge i n c hi l dhood, which re la t e s t o t h e t r a uma o f d e l ive r y.
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Sonuç & Katkı:H e r e , w e r e p o r t e d a n e w b o r n cas e di a g n o s e d w i th mo d e r a te h e m ophi l ia A , w i tho u t t he p re s en c e o f a p ositi v e f a mi l y hi s to r y of h e m ophi l ia an d p re s en t i n g w i th i n t r ac r a n i a l a n d e x t r ac r a n i a l h e m o rr h a g e a n d w e a i m e d to e mph as ize th a t the e a r l y dia g n osis an d r e p l ac e m e n t t h er a py ca rr i e s a n e ss e n tial im p o r t a n c e .
🔬Tür:Olgu Sunumu
📍Kapsam:Genişletilmiş Akademik Örneklem
⚙️Değişkenler:newborn · hemophilia A · intracranial hemorrhage
Abstract
Normal 0 21 false false false TR X-NONE X-NONE /* Style Definitions */ table.MsoNormalTable {mso-style-name:"Normal Tablo"; mso-tstyle-rowband-size:0; mso-tstyle-colband-size:0; mso-style-noshow:yes; mso-style-priority:99; mso-style-qformat:yes; mso-style-parent:""; mso-padding-alt:0cm 5.4pt 0cm 5.4pt; mso-para-margin:0cm; mso-para-margin-bottom:.0001pt; mso-pagination:widow-orphan; font-size:11.0pt; font-family:"Calibri","sans-serif"; mso-ascii-font-family:Calibri; mso-ascii-theme-font:minor-latin; mso-fareast-font-family:"Times New Roman"; mso-fareast-theme-font:minor-fareast; mso-hansi-font-family:Calibri; mso-hansi-theme-font:minor-latin; mso-bidi-font-family:"Times New Roman"; mso-bidi-theme-font:minor-bidi;} In tr ac r a n i a l h e m o r r h a ge a mo n g t e r m n e w b o r n s is a r ar e cl i n i ca l c o n di t ion w i t h high m o rb i dity a n d m o r t al ity. Al though m a jor b le e d i n g is re la tiv e l y u n c om m o n , t h e i nc id en c e of i n t r ac r a n i a l h e m o rr h a g e in h e m ophi l ic c hi l d r e n is hig h e r dur i n g t h e f i r s t f e w d a ys of l ife th a n a t a n y ot h e r s t a ge i n c hi l dhood, which re la t e s t o t h e t r a uma o f d e l ive r y. H e r e , w e r e p o r t e d a n e w b o r n cas e di a g n o s e d w i th mo d e r a te h e m ophi l ia A , w i tho u t t he p re s en c e o f a p ositi v e f a mi l y hi s to r y of h e m ophi l ia an d p re s en t i n g w i th i n t r ac r a n i a l a n d e x t r ac r a n i a l h e m o rr h a g e a n d w e a i m e d to e mph as ize th a t the e a r l y dia g n osis an d r e p l ac e m e n t t h er a py ca rr i e s a n e ss e n tial im p o r t a n c e .
Kader, Ş., Reis, P. G., Mutlu, M., Aslan, Y., Erduran, E., Yazar, U. (2017). A newborn with moderate hemophilia A with severe intracranial and extracranial hemorrhage: A case report. Dicle Tıp Dergisi, Cilt: 44 Sayı: 3, 293–298. https://doi.org/10.5798/dicletip.339025
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