Journals / Marmara Medical Journal / 2003 / Cilt: 16 - Sayı: 3 #67618
HYPERIMMUNOGLOBUUN E SYNDROME (JOB'S SYNDROME) IN A-22-MONTH OLD GIRL AND IVIG TREATMENT
- Journal
- Marmara Medical Journal
- Pages
- 207–210
- DOI
- —
Abstract
Hyperimmunoglobulin E syndrome is a rare disorder characterized by pruritic dermatitis, recurrent staphylococcal skin abscesses and extremely elevated concentrations of immunoglobulin E in serum.We report a patient who has pruritic vesiculopapules, recurrent episodes of skin abscesses on the scalp and face, and respiratory problems from the age of ten days (severe cough, wheezing, acute otitis media, pneumonia). She was diagnosed as Hyper-lgE syndrome and treated with IVIG along with antibiotics.Key Words: Hyperimmunoglobulin Esyndrome, Job’s syndrome
Özet
Hyperimmunoglobulin E syndrome is a rare disorder characterized by pruritic dermatitis, recurrent staphylococcal skin abscesses and extremely elevated concentrations of immunoglobulin E in serum.We report a patient who has pruritic vesiculopapules, recurrent episodes of skin abscesses on the scalp and face, and respiratory problems from the age of ten days (severe cough, wheezing, acute otitis media, pneumonia). She was diagnosed as Hyper-lgE syndrome and treated with IVIG along with antibiotics.Key Words: Hyperimmunoglobulin Esyndrome, Job’s syndrome