Journals / Kocaeli Üniversitesi Sağlık Bilimleri Dergisi / 2017 / Cilt: 3 - Sayı: 1
Hemifacial Microsomia - A Case Report With Review Of Literature
- Pages
- 17–19
- DOI
- —
Abstract
Hemifacial microsomia (HFM) is a congenital deformity characterised by unilateral deficiency in the volume of hard and soft tissue of face. It is a syndrome predominantly affecting first branchial arch featuring poorly developed temporomandibular joint, mandibular ramus, muscles of mastication and ear. People with HFM may present with an underdeveloped ear (microtia) or absent ear (anotia) on the affected side of the face. The incidence of this disorder is 1:3000-26,000, which is usually seen at birth. Here we present a case of hemifacial microsomia in a 12-year-old girl with hearing difficulties on the affected side with review of literature.
Özet
Hemifacial microsomia (HFM) is a congenital deformity characterised by unilateral deficiency in the volume of hard and soft tissue of face. It is a syndrome predominantly affecting first branchial arch featuring poorly developed temporomandibular joint, mandibular ramus, muscles of mastication and ear. People with HFM may present with an underdeveloped ear (microtia) or absent ear (anotia) on the affected side of the face. The incidence of this disorder is 1:3000-26,000, which is usually seen at birth. Here we present a case of hemifacial microsomia in a 12-year-old girl with hearing difficulties on the affected side with review of literature.