Tricuspid Valve Hemangioma Associated with Hypoplastic Left Heart Syndrome Presenting as Sudden Infant Death Syndrome

Abstract

Primary cardiac tumors are rare in children with a low incidence varying from 0.0017 to 0.28% in autopsy studies. Approximately 90% ofthe reported primary cardiac tumors in the pediatric population are benign and the most common subtype is rhabdomyomas accounting forapproximately 60%, while hemangiomas are rare primary tumors with a 5% incidence. Hypoplastic left heart syndrome is abnormal developmentof the left-sided cardiac structures, leading to obstruction of blood flow from the left ventricle out-flow tract. Here we report a case of tricuspidhemangioma in association with hypoplastic left heart syndrome, a rare association not previously reported in the literature.