Posterior Polar Central Choroidal Dystrophy: A Case Report

Abstract

A 52-year-old male presented with a 25-year history of decreasing vision. Best corrected visual acuity was 0.3 in his right and 0.2 inhis left eye. Fundoscopic examination showed bilateral symmetric atrophy of the retinal pigment epithelium and choriocapillaris in theposterior polar areas between vascular arcades and surrounding the optic disc. On fluorescein angiography, the large choroidal vesselsbeneath these affected regions were easily seen. Fundus autofluorescence imaging showed clearly defined hypoautofluorescent areas thatcorresponded to the aforementioned lesions. Atrophy of the choriocapillaris and outer retinal layer were detected in optical coherencetomography. Photopic and scotopic responses were subnormal in flash electroretinogram (ERG), and responses were also minimal inpattern ERG and multifocal ERG. The patient was diagnosed with posterior polar central choroidal dystrophy. We aimed to present theresults of fluorescein angiography, fundus autofluorescence imaging, optical coherence tomography, and electrophysiological tests in thisrare case of posterior polar central choroidal dystrophy.