Bilateral Asymmetric Rhegmatogenous Retinal Detachment in a Patient with Stickler Syndrome

Abstract

Here we present the long-term anatomical and visual outcomes of bilateral asymmetric rhegmatogenous retinal detachment repair ina patient with Stickler syndrome. A 17-year-old girl presented with decreased visual acuity in both eyes for more than one year. Herbest-corrected visual acuity (BCVA) was 0.1 in the right eye and 0.05 in the left eye. Slit-lamp anterior segment examination revealedsubcapsular cataract in both eyes. Fundus examination showed bilateral rhegmatogenous retinal detachment, chronic retinal detachmentaccompanied by multiple retinal holes, tears and membranous fibrillary vitreous in the peripheral retina. Grade C2 proliferativevitreoretinopathy was observed in the left eye. Scleral buckling surgery was performed initially for both eyes. After the primarysurgical procedure, retinal reattachment was achieved in the right eye and the left eye underwent phacoemulsification, intraocular lensimplantation, pars plana vitrectomy (PPV), and silicone oil injection. After these surgical procedures retinal reattachment was achievedin the left eye. Silicone oil removal was performed six months after PPV surgery. After surgical treatment, BCVA was 0.6 in the righteye at the end of the 3.5-year follow-up period. After silicone oil removal, BCVA reached 0.2 in the left eye after 36 months of follow-upand retinal reattachment was achieved in both eyes. Scleral buckling surgery and PPV are effective and confidential methods for thetreatment of chronic retinal detachment cases in Stickler syndrome.