Stage 1 hybrid palliation of hypoplastic left heart syndrome: an initial experience in pulmonary trunk approach, procedural modifications, and complication management

Abstract

Background/aim: Hypoplastic left heart syndrome (HLHS) is a rare pathology with a very high mortality rate. The present study aimedto share our initial experience with the ductus arteriosus stenting procedure using the pulmonary trunk approach in the treatment ofHLHS, as well as provide some technical suggestions and discuss complications and their management.Materials and methods: The medical records of 9 neonates (age range: 1–8 days) with HLHS, who were operated on within a12-month period, were reviewed retrospectively. Preprocedural planning was performed by computed tomography angiography andechocardiography. The operations were performed in a hybrid surgery room by interventional radiologists and pediatric vascularsurgeons. Balloon-expandable stents were used in all of the operations.Results: All operations were successfully completed without any intraoperative mortality. All intraoperative complications weremanaged successfully during the stenting procedure.Conclusion: Stage 1 hybrid palliation for HLHS is a safe and effective procedure when several key points are kept in mind.