Dyke–Davidoff–Masson Syndrome: A Case with Electroencephalography and Lesion Discordance

Abstract

Dyke–Davidoff–Masson Syndrome (DDMS) is a rare syndrome characterized by cerebral hemiatrophy, hyperpneumatization of the paranasal sinuses, homolateral skull hyperplasia, seizures that may be associated with mental retardation, and contralateral hemiparesis. Focal onset seizures may be seen in patients. Interictal Electroencephalogram (EEG) recordings of these patients were evaluated as lower amplitude and slow background activity in the affected hemispheres. While most of the cases have lateralized epileptiform disorder com- patible with the lesion, cases with continuous discordance in EEG are rarely presented in the literature. Epileptiform discordance occurs infrequently, as in our case; it is crucial to keep this in mind when finding irritative areas, particularly in patients with big lesions. We aimed to discuss a patient who had epileptiform discordance and was diagnosed with DDMS, which is an uncommon condition in the literature, and examine the literature based on this case.