Journals / Respiratory Case Reports / 2021 / Cilt: 10 - Sayı: 2
Pulmonary Arterial Hypertension in a Patient with Connective Tissue Disease and ALCAPA Syndrome
- Journal
- Respiratory Case Reports
- Pages
- 92–94
- DOI
- —
Abstract
A 43-year-old female with mixed connective tissue disease was incidentally discovered to be an adult survivor of an anomalous left coronary artery origi- nating from the pulmonary artery during a work-up for her pulmonary hypertension. We describe here the management strategy of severe pulmonary hyperten- sion prior to and after the surgical correction of the congenital anomaly.
Özet
Mikst konnektif doku hastalığı olan 43 yaşındaki kadında, pulmoner arteriyel hipertansiyon araştırma- ları sırasında, yaşayan bir yetişkinde, pulmoner arter- den orijin alan sol koroner arter anomalisi saptandı. Konjenital anomalinin cerrahi tedavisi öncesi ve son- rası, ciddi pulmoner hipertansiyon yönetim stratejisini açıklıyoruz.