Papillon-lefévre syndrome: Report of two cases

Abstract

Papillon-Lefevre syndrome is a rare genetic disorder characterised by palmar-plantar hyperkeratosis and severe periodontitis. Here reported two cases of Papillon-Lefevre syndrome, aged 16 and 6 years, one of whom was previously misdiagnosed as psoriasis vulgaris and was treated successfully with acitretin. The other responded very well to topical emollients.