Wegener's granulomatosis presenting with an ısolated paranasal sinus ınvolvement in a child

Abstract

Wegener s granulomatosis which is rarely seen in children is an idiopathic necrotizing granulomatous vasculitis, affecting primarily paranasal sinuses, nasopharynx, lungs, kidneys and joints. In this article, we report a very rare case of eight-year-old boy presenting with Wegener s granulomatosis of paranasal sinuses without lung, kidney and any other organ involvement. We discuss the diagnosis, treatment and the differential diagnosis of paranasal sinus involvement in Wegener s granulomatosis in the light of literature data.