LIMB-GIRDLE MUSKÜLER DISTROFILI OBSTETRIK HASTADA ANESTEZI YÖNETIMI: VAKA TAKDIMI VE LITERATÜR TARAMAS

Anesthetic Management of an Obstetric Patient with Limb-Girdle Muscular Dystrophy: Case Report and Review of the Literature

Özet

Limb-girdle musküler distrofi zor havayolu, kas zayıflığı, artmış pulmoner aspirasyon riski, kardiomyopati ve rabdomyoliz gibi tehlikeli sistemik komponentleri olan, genetik geçişli, seyrek görülen bir hastalıktır. Bu vakada, Limb girdle musküler distrofili 36 yaşında bir gebenin spinal anestezi ile acil sezaryeni sırasındaki anestezi yönetimini ve literatürdeki obstetrik Limb-girdle musküler distrofi hastalarını gözden geçirmeyi amaçladık.

Abstract

Limb-girdle muscular dystrophy is a rare hereditary disease with dangerous systemic components including difficult airway, muscle weakness, increased risk for pulmonary aspiration, cardiomyopathy, and rhabdomyolysis that make anesthetic management challenging. In this case report, we aimed to discuss the anesthetic management of a 36-year-old pregnant woman with Limb-Girdle Muscular Dystrophy (LGMD) who underwent emergent caesarean section with spinal anesthesia and to review of the anesthetic management of obstetricLimb-Girdle patients in the literature.