Journals / Romatizma Dergisi / 2002 / Cilt: 17 - Sayı: 2
A case report: Osteopoikilosis with undifferentiated connective tissue disease, livedoid vasculitis and antiphospholipid syndrome
- Journal
- Romatizma Dergisi
- Pages
- 124–129
- DOI
- —
Abstract
Osteopoikilosis, which belongs to the group of osteosclerotic diseases, has an autosomal dominant inheritance. Having typical radiological findings and asymptomatic clinical course, 15-20% of cases may experience mild articular tenderness and effusions. Osteopoikilosis associated with a connective tissue disease and/or livedoid vasculitis and/or antiphospholipid syndrome has not been reported yet. Here, a patient with undifferentiated connective tissue disease, livedoid vasculitis, antiphospholipid syndrome and osteopoikilosis will be discussed.
Özet
Osteosklerotik hastalıklar arasında yer alan osteopoikiloz tipik radyolojik bulguları olan asemptomatik seyirli otozomal dominant geçen bir hastalıktır. % 15-20 olguda hafif artiküler ağrılar ve eklem efüzyonu olabilir. Şimdiye kadar osteopoikiloza eşlik eden bağ dokusu hastalığı ve/veya livedoid vaskülit ve/veya antifosfolipid sendromu birlikteliği bildirilmemiştir. Andifferansiye bağ dokusu hastalığı, livedoid vaskülit, antifosfolipid sendromu ve osteopoikiloz tanıları alan hasta tartışılacaktır.