AI Summary & Key Takeaways
AI InsightIn this case presentation, a 29 year old male patient who has sickle cell anemia and who has been experiencing pain and difficulty in walking for a month is chosen.
📌 3 Key Takeaways
Abstract
Sicklecellanemia is defined as a hereditary disease which is caused by abnormal hemoglobins that are called hemoglobin S. In sickle cell anemia crisis, generally infarction develops as a result of the blockage of capillaries in the chest, bones and abdomen by the erythrocytes with damaged morphology. In this case presentation, a 29 year old male patient who has sickle cell anemia and who has been experiencing pain and difficulty in walking for a month is chosen. Sicklecellanemia is defined as a hereditary disease which is caused by abnormal hemoglobins that are called hemoglobin S. In sickle cell anemia crisis, generally infarction develops as a result of the blockage of capillaries in the chest, bones and abdomen by the erythrocytes with damaged morphology. In this case presentation, a 29 year old male patient who has sickle cell anemia and who has been experiencing pain and difficulty in walking for a month is chosen.
Özet
Orak hücreli anemi (Sicklecellanemia) hemoglobin S olarak adlandırılan anormal hemoglobinlerin sebeb olduğu herediter geçişli hastalık olarak tanımlanmaktadır. Orak hücre anemi krizinde genellikle göğüste, kemiklerde ve abdomendeki kapillerlerin morfolojisi bozulmuş eritrositler tarafından tıkanmasıyla meydana gelen infarktlar oluşur. Bu vaka takdimindeorak hücre anemisi bulunan ve bir aydır devam eden yürümekte zorluk ve ağrı şikayeti bulunan 29 yaşında erkek hasta sunulmuştur.Orak hücreli anemi (Sicklecellanemia) hemoglobin S olarak adlandırılan anormal hemoglobinlerin sebeb olduğu vasooklisiv, aplastik ve hemolitik krizlere yol açabilen herediter geçişli bir hastalıktır (1). Orak hücreli anemide akut (ağrılı vasooklisiv kriz) ve kronik olarak (avaskuler nekrozun progresiv olarak ilerlemesi) kemik tutulumu en sık karşılaşılan komplikasyonlardan biridir (2).