Journals / Journal of Surgery and Medicine / 2019 / Cilt: 3 - Sayı: 8

Use of video-laryngoscopy in pediatric patients with Ehlers-Danlos syndrome: Two case reports

Ehlers-Danlos sendromu tanılı iki pediatrik hastada videolaringoskop kullanımı: İki olgu sunumu

Pages
626–628
Publication Date
2019-08-01
DOI
—
🏛️Bibliographic metadata and full text access for this article are provided via DergiPark.
DergiPark Record ↗
✨

AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

We believe that using video-laryngoscopy for managing difficult pediatric airways may be beneficial in avoiding complications.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Difficult airway management is one of the most challenging situations for an anesthesiologist.
📊
Key Findings & Data:The first case was a 9-year-old, male, ASA II EDS patient scheduled for strabismus surgery, and the second case was a 12-year-old, male, ASA III EDS patient who was also diagnosed with a brain cyst and lymphoma, due for emergency surgery for acute abdomen.
💡
Conclusion & Impact:We believe that using video-laryngoscopy for managing difficult pediatric airways may be beneficial in avoiding complications.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Ehlers-Danlos · Anestezi · Zor hava yolu

Abstract

Difficult airway management is one of the most challenging situations for an anesthesiologist. If not handled properly, it can lead to severe complications, even death. Video-laryngoscopy (VL) is one of the many techniques developed for this purpose. Ehlers-Danlos Syndrome (EDS) is a rare disease requiring possible difficult airway management due to temporo-mandibular dysfunction or occipito-atlanto-axial instability. We herein present two pediatric EDS cases who required surgery. The first case was a 9-year-old, male, ASA II EDS patient scheduled for strabismus surgery, and the second case was a 12-year-old, male, ASA III EDS patient who was also diagnosed with a brain cyst and lymphoma, due for emergency surgery for acute abdomen. With their heads in a neutral position, both patients were intubated without tissue trauma at first attempt using video-laryngoscopy. No complications were encountered in both cases. We believe that using video-laryngoscopy for managing difficult pediatric airways may be beneficial in avoiding complications.

Özet

Zor hava yolu yönetimi, anestezist için en problemli durumlardan biridir ve komplikasyonlara, hatta ölüme neden olabilir. Videolaringoskop, bu sebeple geliştirilen tekniklerden birisidir. Ehlers-Danlos Sendromu, temporomandibular disfonksiyon veya oksipito-atlanto-aksiyel instabilite nedeniyle zor hava yolu yönetimine ihtiyaç duyulabilen nadir bir hastalıktır. Burada Ehlers-Danlos Sendromu (EDS) tanılı iki olgu sunulmuştur. İlk olgu, 12 yaşında, ASA II, EDS tanılı, strabismus nedeniyle cerrahi planlanan erkek hasta, ikinci olgu ise 9 yaşında, ASA III, EDS, beyin kisti ve lenfoma tanılı, akut batın sebebiyle acil cerrahiye ihtiyacı doğan erkek hastadır. Her iki hasta, başları nötral pozisyondayken, dokuyu travmatize etmeden, video-laringoskop ile ilk denemede entübe edilmiştir ve herhangi bir komplikasyonla karşılaşılmamıştır. Olası komplikasyonlardan kaçınmak için pediatrik zor hava yolu yönetiminde video-laringoskop kullanımının faydalı olacağını düşünüyoruz.

🔖

Cite This Article

EROL, M. K., KAYA, F. (2019). Use of video-laryngoscopy in pediatric patients with Ehlers-Danlos syndrome: Two case reports. Journal of Surgery and Medicine, Cilt: 3 - Sayı: 8, 626–628. https://ajindex.com/articles/780527

📄 Full Text PDF Viewer

📄

PDF görüntüleyici hazırlanıyor...

References (13)

  1. Callewaert B, Malfait F, Loeys B, De Paepe A. Ehlers-danlos syndromes and Marfan syndrome. Best Pract Res Clin Rheumatol. 2008;22:165–89
  2. Halko GJ, Cobb R, Abeles M. Patients with type IV ehlers-danlos syndrome may be predisposed to atlantoaxial subluxation. J Rheumatol. 1995;22:2152–5
  3. Johnston BA, Occhipinti KE, Baluch A, Kaye AD. Ehlers-Danlos Syndrome: Complications And Solutıons Concerning Anesthetic Management. Middle East Journal Anaesthesiology. 2006;18(6):1171-84
  4. Wiesmann T, Castori M, Malfait F, and Wulf H. Recommendations for anesthesia and perioperative management in patients with Ehlers-Danlos syndrome(s) Orphanet J Rare Dis. 2014;9:109
  5. Uitto J, Ringpfell F. Ehlers-Danlos Syndrome-Molecular Genetics, Beyond the Collagens. The Society for Investigative Dermatology. 2004;122:4
  6. Beighton P, De Paepe A, Steinmann B, Tsipouras P, Wenstrup RJ. Ehlers-Danlos syndromes: revised nosology. Am J Med Genet. 1998;77:31-7
  7. Campbell N, Rosaeg OP. Anesthetic management of a parturient with Ehlers Danlos syndrome type IV. Can J Anaesth. 2002;49(5):493-6
  8. De Paepe A, Malfait F. Bleeding and bruising in patients with Ehlers-Danlos syndrome and other collagen vascular disorders. British Journal of Haematology. 2004;127:491-500
  9. Germain DP. Ehlers-Danlos syndrome type IV. Orphanet Journal of Rare Diseases. 2007;2:1-9 10. Sood V, Robinson DA, Suri I. Difficult intubation during rapid sequence induction in a parturient with Ehlers-Danlos syndrome, hypermobility type. Int J Obstet Anesth. 2009;18:408-12
  10. Yen J, Lin SP, Chen MR, Niu DM. Clinical features of Ehlers Danlos syndrome. J Formos Med Assos. 2006;105:475-80
  11. Ohshita N. Kanazumi M, Tsuji K, Yoshida H, Morita S, Momota Y, et al. Anesthetic Management of a Patient With Ehlers-Danlos Syndrome. Anesth Prog. 201;63(4):204-7
  12. Jiang J, MA Dx, Li B, Wu As, Xue Fs. Videolryngoscopy versus direct laryngoscopy for nasotracheal intubation: A systematic review of randomised control trials. Journal of Clinical Anesthesia. 2019;52(12):6-16 14. Watt S, Kalpan J, Kolli V. Case report of the use of videolaryngoscopy in thyroid goiter masses:An airway challenge. Int J Surg Case Rep. 2016;27:119-21. doi: 10.1016/j.ijscr.2016.06.018
  13. Madziala M, Smereka J, Dabrowski M, Leung S, Ruetzler K, Szarpak L. A comparison of McGrath MAC and standard direct laryngoscopy in simulated immobilized cervical spine pediatric intubation: a manikin study. Eur J Pediatr. 2017;176(6):779-86.