Factor 8, von Willebrand factor antigen, and von Willebrand Ristocetin cofactor levels were significantly lower in patients with PBS≥2 compared to those in patients with PBS
📌 3 Key Takeaways
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Objective & Hypothesis:Aim: Epistaxis may be a symptom of an inherited bleeding disease..
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Key Findings & Data:We aimed to analyze an approved pediatric bleeding score (PBS) as a screening test for von Willebrand Disease (VWD) in children with epistaxis Material and Method: We retrospectively reviewed the medical records of pediatric patients, who applied to the Pediatric Hematology Department with the complaint of epistaxis between January 2018 and December 2019.
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Conclusion & Impact:Factor 8, von Willebrand factor antigen, and von Willebrand Ristocetin cofactor levels were significantly lower in patients with PBS≥2 compared to those in patients with PBS
🔬Design:Review & Systematic Survey
📍Scope:2018 Verileri
⚙️Variables:Pediatric bleeding score · Epistaxis · Von Willebrand Disease
Abstract
Aim: Epistaxis may be a symptom of an inherited bleeding disease.. We aimed to analyze an approved pediatric bleeding score (PBS) as a screening test for von Willebrand Disease (VWD) in children with epistaxis Material and Method: We retrospectively reviewed the medical records of pediatric patients, who applied to the Pediatric Hematology Department with the complaint of epistaxis between January 2018 and December 2019. Results: One hundred and sixty eight patients enrolled in this study There were 65(38.7%) girls and 103(61.3%) boys, with a mean age of 114±49 months (range 8 months to 18 years).The PBS of 34 patients was greater than/ or equal to 2. Factor 8, von Willebrand factor antigen, and von Willebrand Ristocetin cofactor levels were significantly lower in patients with PBS≥2 compared to those in patients with PBS
ALPCAN, A., TURSUN, S., KANDUR, Y., YÖRGÜÇ, M. Ç., ALBAYRAK, M. (2022). The predictive value of bleeding score on the diagnosis of Von Willebrand disease in children applied to the hematologic clinic with epistaxis. Journal of Health Sciences and Medicine, Cilt: 5 - Sayı: 1, 22–25. https://ajindex.com/articles/776637
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