Diagnostic Imaging of Lymphangiomatosis- A Pictorial Overview

Objective & Hypothesis:Lymphangiomatosis is a rare congenital disorder, characterized by a diffuse proliferation of lymphatic channels involving bones, parenchymal organs, and soft tissue.

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Key Findings & Data:Lymphangiomatosis frequently presents in late childhood.

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Conclusion & Impact:We present the clinical and imaging features of a 14-year old girl with lymphangiomatosis and particularly involvement of mandible.

🔬Design:Research Article

📍Scope:Comprehensive Sample

⚙️Variables:lenfanjiomatozis · mandibula · lenfanjiyom

Abstract

Lymphangiomatosis is a rare congenital disorder, characterized by a diffuse proliferation of lymphatic channels involving bones, parenchymal organs, and soft tissue. Lymphangiomatosis frequently presents in late childhood. It produces lytic lesions in multiple bones. Prognosis of the disease has been variously reported from benign to fatal. We present the clinical and imaging features of a 14-year old girl with lymphangiomatosis and particularly involvement of mandible.

Özet

Lenfanjiomatozis; kemikler, parankimal organlar ve yumuşak dokuyu kapsayan lenf kanallarının diffüz proliferasyonu ile karakterize nadir görülen konjenital bir bozukluktur. Lenfanjiomatozis sıklıkla geç çocuklukta görülür. Birden çok kemiklerde litik lezyonlar oluşturur. Hastalığın prognozu iyi huylu durumdan ölümcül hale kadar çeşitli şekillerde rapor edilmiştir. Biz özellikle mandibula tutulumu olan lenfanjiomatozisli 14 yaşındaki bir kız klinik ve görüntüleme bulguları sunuldu.

Keywords

lenfanjiomatozis mandibula lenfanjiyom Lymphangiomatosis mandible lymphangioma

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Cite This Article

HEGDE, S., UPADHYAYA, V., BN, P., AR, S., BABU, S., SHETTY, S. R., AJİLA, V. (2012). Diagnostic Imaging of Lymphangiomatosis- A Pictorial Overview. Journal of Contemporary Medicine, Cilt: 2 - Sayı: 2, 105–108. https://ajindex.com/articles/775750

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