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Journals / Journal of Contemporary Medicine / 2014 / Cilt: 4 - Sayı: 2 EK

Arthrogrypozis Multiplex Congenita and Anesthesia: A Case Report and Review of the Literature

Artrogripozis Multipleks Konjenita ve Anestezi: Olgu Sunumu ve Literatürün Gözden Geçirilmesi

Serkan KARAMAN
Tuğba KARAMAN
Serkan DOĞRU
Aynur ŞAHİN
Hakan TAPAR
Pages
100–14
Publication Date
2014-09-09
DOI
—
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

In this case report, we aimed to present the anesthesia management of a 13 months-old case with arthrogryposis multiplex congenita who operated for joint contracture.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Arthrogryposis Multiplex Congenita is a term that describes a rare congenital syndrome.
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Key Findings & Data:Clinical features is characterized by multiple joint contractures that requires recurrent surgical interventions.
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Conclusion & Impact:In this case report, we aimed to present the anesthesia management of a 13 months-old case with arthrogryposis multiplex congenita who operated for joint contracture.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Artrogripozis multipleks konjenita · anestezi · genel

Abstract

Arthrogryposis Multiplex Congenita is a term that describes a rare congenital syndrome. Clinical features is characterized by multiple joint contractures that requires recurrent surgical interventions. Various system anomalies can be associated with this syndrome. The anesthesia management of a patient with Arthrogryposis Multiplex Congenita may lead to several challenges including difficult airway, difficult venous access and malign hyperthermia. In this case report, we aimed to present the anesthesia management of a 13 months-old case with arthrogryposis multiplex congenita who operated for joint contracture.

Özet

Artrogripozis multipleks konjenita nadir görülen bir konjenital sendromu tanımlayan terimdir. Klinik tablo, tekrarlayan cerrahi girişimler gerektiren multipl eklem kontraktürleriyle karakterizedir. Çeşitli sistem anomalileri bu sendroma eşlik edebilir. Artrogripozis multipleks konjenitalı hastada anestezi yönetimi; zor havayolu, zor damaryolu ve malign hipertermiyi içeren birçok zorluğa yol açabilir. Biz bu olgu sunumunda, eklem kontraktürü için opere edilen 13 aylık erkek çocuğunun anestezi yönetimini tartışmayı amaçladık.

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Cite This Article

KARAMAN, S., KARAMAN, T., DOĞRU, S., ŞAHİN, A., TAPAR, H. (2014). Arthrogrypozis Multiplex Congenita and Anesthesia: A Case Report and Review of the Literature. Journal of Contemporary Medicine, Cilt: 4 - Sayı: 2 EK, 100–14. https://ajindex.com/articles/775645

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References (9)

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