Anesthetic considerations of 7 months old girl with Beckwith- Wiedemann syndrome during reduction of macroglossia are presented and discussed.
📌 3 Key Takeaways
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Objective & Hypothesis:The Beckwith-Wiedemann syndrome is characterized by macroglossia; pre- or postnatal gigantism; abdominal wall defects; hypoglycaemia; umbilical hernia or diastasis recti; ear creases or posterior helical ear pits; facial nevus flammeus; renal anomalies; neoplasms; hemihypertrophy; congenital cardiac malformations; intestinal malrotation; mental retardation; polydactyly; and cleft palate.
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Key Findings & Data:The Beckwith-Wiedemann syndrome is characterized by macroglossia; pre- or postnatal gigantism; abdominal wall defects; hypoglycaemia; umbilical hernia or diastasis recti; ear creases or posterior helical ear pits; facial nevus flammeus; renal anomalies; neoplasms; hemihypertrophy; congenital cardiac malformations; intestinal malrotation; mental retardation; polydactyly; and cleft palate.
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Conclusion & Impact:Anesthetic considerations of 7 months old girl with Beckwith- Wiedemann syndrome during reduction of macroglossia are presented and discussed.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters
Abstract
The Beckwith-Wiedemann syndrome is characterized by macroglossia; pre- or postnatal gigantism; abdominal wall defects; hypoglycaemia; umbilical hernia or diastasis recti; ear creases or posterior helical ear pits; facial nevus flammeus; renal anomalies; neoplasms; hemihypertrophy; congenital cardiac malformations; intestinal malrotation; mental retardation; polydactyly; and cleft palate. Anesthetic considerations of 7 months old girl with Beckwith- Wiedemann syndrome during reduction of macroglossia are presented and discussed.
Özet
Beckwith-Weidemann sendromu makroglossi; pre veya postnatal jigantizm; abdominal duvar defekti; hipoglisemi; umbilical herni veya diastazis rekti; kulak kepçesinde kıvrılmalar veya posterior helical pitler; fasial nevus flammeus; renal anomaliler; neoplasmlar; hemihipertrofi; konjenital kardiyak malformasyonlar; intestinal malrotasyon; mental retardasyon; polidaktili ve yarık damak ile karakterizedir. Bu yazıda Beckwith-Weidemann sendrom'lu, 7 aylık kız çocukta, makroglossi küçültme operasyonu için verilen anestezi uygulaması bildirilmiştir.
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Cite This Article
BİÇER, C., AKSU, R., ESKİTAŞÇIOĞLU, T., MADENOĞLU, H. (2022). Beckwith-weidemann sendromlu büyük dili olan vakada anestezi yönetimi. Erciyes Tıp Dergisi, Cilt: 33 - Sayı: 3, 251–254. https://ajindex.com/articles/650121
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