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Journals / Türk Patoloji Dergisi / 2018 / Cilt: 34 - Sayı: 3

Congenital Complete Tracheal Ring in a Neonate: A Case Report

Senem ALKAN ÖZDEMİR
Esra ARUN ÖZER
Sümer SÜTÇÜOĞLU
Süheyla CUMURCU
Özkan İLHAN
Ümit BAYOL
Pages
259–261
Publication Date
2022-11-05
DOI
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

Here, we report an extreme case of VACTErL/TACrD association presented with congenital complete tracheal ring, encephalocele, bilateral radial agenesis with absent thumbs, equinovalgus deformity on right foot, low-set ears and micrognathia.

📌 3 Key Takeaways

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Objective & Hypothesis:Abnormalities of the upper airway tract lead to congenital high airway obstruction and may complicate neonatal airway management in the delivery room.
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Key Findings & Data:Congenital complete tracheal rings are a rare and unusual tracheal anomaly, usually presenting in the neonate or infant as respiratory distress.
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Conclusion & Impact:Here, we report an extreme case of VACTErL/TACrD association presented with congenital complete tracheal ring, encephalocele, bilateral radial agenesis with absent thumbs, equinovalgus deformity on right foot, low-set ears and micrognathia.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

Abnormalities of the upper airway tract lead to congenital high airway obstruction and may complicate neonatal airway management in the delivery room. Congenital complete tracheal rings are a rare and unusual tracheal anomaly, usually presenting in the neonate or infant as respiratory distress. The clinical presentation can vary from almost asymptomatic patients to near-fatal airway obstruction. It may exist as an isolated entity, or in association with other congenital malformations, in particular, cardiac anomalies along with vascular rings and pulmonary slings. Other associated anomalies have also been reported, for example, chromosomal anomalies, malformation of other parts of the respiratory tract, esophagus and skeletal systems. Here, we report an extreme case of VACTErL/TACrD association presented with congenital complete tracheal ring, encephalocele, bilateral radial agenesis with absent thumbs, equinovalgus deformity on right foot, low-set ears and micrognathia.

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Cite This Article

ÖZDEMİR, S. A., ÖZER, E. A., SÜTÇÜOĞLU, S., CUMURCU, S., İLHAN, Ö., BAYOL, Ü. (2022). Congenital Complete Tracheal Ring in a Neonate: A Case Report. Türk Patoloji Dergisi, Cilt: 34 - Sayı: 3, 259–261. https://ajindex.com/articles/640500

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