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Journals / Türkiye Acil Tıp Dergisi / 2012 / Cilt: 12 - Sayı: 1

A case of hereditary angioedema presenting with larynx edema

Larenks ödemi ile seyreden bir herediter anjioödem olgusu

Ayhan SARITAŞ
Ali KUTLUCAN
Hakan TURAN
Faruk ÇEÇEN
Mehmet Emin YANIK
Pages
45–47
Publication Date
2022-11-05
DOI
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

Herein, we present a male hereditary angioedema case with laryngeal edema which is severe enough to require tracheostomy.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Hereditary angioedema is a rare and potentially life-threatening disease resulting from deficiency or disfunction of C1 esterase inhibitor which is produced by hepatocytes.
📊
Key Findings & Data:It is characterized by recurrent angioedema attacks at subcutaneous or submucosal region.
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Conclusion & Impact:Herein, we present a male hereditary angioedema case with laryngeal edema which is severe enough to require tracheostomy.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

Hereditary angioedema is a rare and potentially life-threatening disease resulting from deficiency or disfunction of C1 esterase inhibitor which is produced by hepatocytes. It is characterized by recurrent angioedema attacks at subcutaneous or submucosal region. Larynx edema could be seen rarely in hereditary angioedema and may result in death by causing sudden air way obstruction. Herein, we present a male hereditary angioedema case with laryngeal edema which is severe enough to require tracheostomy.

Özet

Herediter anjioödem hepatositler tarafından üretilen C1 esteraz inhibitör eksikliği veya disfonksiyonundan kaynaklanan, nadir rastlanılan, potansiyel olarak yaşamı tehdit edici bir hastalıktır. Subkutan veya submukozal bölgede tekrarlayan anjioödem ataklarıyla karakterizedir. Herediter anjioödemde nadir olarak görülen larenks ödemi ani hava yolu obstruksiyonuna neden olup ölümle sonuçlanabilir. Burada trakeostomi açılmasını gerektirecek kadar şiddetli larenks ödemi gelişen herediter anjioödemli bir erkek olgu sunulmaktadır.

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Cite This Article

SARITAŞ, A., KUTLUCAN, A., TURAN, H., ÇEÇEN, F., YANIK, M. E. (2022). A case of hereditary angioedema presenting with larynx edema. Türkiye Acil Tıp Dergisi, Cilt: 12 - Sayı: 1, 45–47. https://ajindex.com/articles/625969

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References (9)

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