Acute necrotizing encephalopathy of childhood: a Turkish case

Objective & Hypothesis:Acute necrotizing encephalopathy of childhood (ANEC) is a rare form of acute encephalopathy of unknown etiology characterized by typical symmetrical lesions in the thalami, with variable involvement of the white matter, brainstem and cerebellum.

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Key Findings & Data:Here we present a 3-year-old boy admitted to our hospital with fever and deterioration of consciousness.

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Conclusion & Impact:The diagnosis of ANEC was made by radiologic findings

🔬Design:Research Article

📍Scope:Comprehensive Sample

⚙️Variables:akut nekrotizan ensefalopati · çocukluk çağı · parainfluenza virus

Abstract

Acute necrotizing encephalopathy of childhood (ANEC) is a rare form of acute encephalopathy of unknown etiology characterized by typical symmetrical lesions in the thalami, with variable involvement of the white matter, brainstem and cerebellum. Clinically there is a rapid neurologic deterioration after a short period of a nonspecific viral-like illness associated with gastrointestinal or respiratory signs. Asian children are especially affected. Here we present a 3-year-old boy admitted to our hospital with fever and deterioration of consciousness. The diagnosis of ANEC was made by radiologic findings

Özet

Çocukluk çağının akut nekrotizan ensefalopatisi, talamusta tipik, simetrik lezyonlarla, ak madde, beyin sapı ve serebellumun değişken tutulumuyla nitelenen, etiyolojisi bilinmeyen, nadir bir akut ensefalittir. Klinikte, gastrointestinal veya solunum sistemini etkileyen viral enfeksiyonlar sonrasında hızlı nörolojik bozulma izlenir. Asya kökenli çocuklarda daha sık görülür. Bu yazıda, bilinç bulanıklığı, ve ateş nedeniyle hastanemize başvuran, akut nekrotizan ensefalopati tanısı radyolojik bulgular ile konulan 3 yaşında bir erkek olgu sunuldu

Keywords

akut nekrotizan ensefalopati çocukluk çağı parainfluenza virus acute necrotizing encephalopathy children

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Cite This Article

ÜNVER, O., HASILOĞLU, Z. İ., ŞAHİN, S., ALBAYRAM, M. S., TAŞTAN, Y. (2014). Acute necrotizing encephalopathy of childhood: a Turkish case. Cukurova Medical Journal, Cilt: 39 - Sayı: 3, 641–645. https://ajindex.com/articles/56989

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