Papillary intralymphatic angioendothelioma: An extremely rare tumor

Key Findings & Data:In this article, we present a 12-year-old male patient with a PILA treated with re-excision, skin grafting, and sentinel lymph node biopsy.

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Conclusion & Impact:Frequent examination of lymph nodes and skin lesion also might be beneficial during the follow-ups.

🔬Design:Research Article

📍Scope:Comprehensive Sample

⚙️Variables:Domain Parameters

Abstract

Papillary intralymphatic angioendothelioma (PILA), an intralymphatic lesion of vascular ducts, is an extremely rare tumor. It is generally encountered as an unexpected pathology following excision of a vascular skin lesion. Re-excision is the commonly preferred treatment option once the pathological diagnosis is established. In this article, we present a 12-year-old male patient with a PILA treated with re-excision, skin grafting, and sentinel lymph node biopsy. The patient was symptom-free at annual follow-up. A sentinel lymph node biopsy during re-excision might be a good option in the surgical management of PILA. Frequent examination of lymph nodes and skin lesion also might be beneficial during the follow-ups.

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Cite This Article

ÖZGÜR, F., ORHAN, D., KAPLAN, G. O., ÖZDEMİR, F. D. M., AKSU, A. E. (2022). Papillary intralymphatic angioendothelioma: An extremely rare tumor. Joint diseases and related surgery, Cilt: 32 - Sayı: 1, 245–248. https://ajindex.com/articles/559248

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