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Journals / İstanbul Kuzey Klinikleri / 2018 / Cilt: 5 - Sayı: 1

Renal Clear Cell Sarcoma Presenting as a Spontaneous Renal Hematoma: A Rare Presentation

Özcan BOR
Zeynep Canan ÖZDEMİR
Mehmet Surhan ARDA
Burcu AYVACI
Yeter DÜZENLİ KAR
Mehmet OĞUZMAN
Mustafa Fuat AÇIKALIN
Pages
60–63
Publication Date
2022-10-18
DOI
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

CCSK should be kept in mind in the differential diagnosis of a renal mass.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Clear cell sarcoma of the kidney (CCSK) is an uncommon renal neoplasm of childhood.
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Key Findings & Data:It represents between 2% and 9% of all pediatric renal tumors, and generally arises before the age of 5 years.
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Conclusion & Impact:CCSK should be kept in mind in the differential diagnosis of a renal mass.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

Clear cell sarcoma of the kidney (CCSK) is an uncommon renal neoplasm of childhood. It represents between 2% and 9% of all pediatric renal tumors, and generally arises before the age of 5 years. It often mimics other pediatric renal tumors. Presently described is the case of a 7-year-old girl who presented with complaints of vomiting and abdominal pain. Abdominal ultrasonography revealed a right renal mass, and the patient developed a renal hematoma a few hours after admission. The patient underwent a nephroureterectomy with a provisional diagnosis of Wilms tumor; however, histopathological examination of a specimen revealed CCSK. CCSK is similar to Wilms tumor in terms of the typical age of appearance and clinical and histopathological features, but the treatment method and prognosis are different. Therefore, the differential diagnosis is very important. This case was presented to draw attention to a rare presentation of clear cell sarcoma. CCSK should be kept in mind in the differential diagnosis of a renal mass.

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Cite This Article

BOR, Ö., ÖZDEMİR, Z. C., ARDA, M. S., AYVACI, B., KAR, Y. D., OĞUZMAN, M., AÇIKALIN, M. F. (2022). Renal Clear Cell Sarcoma Presenting as a Spontaneous Renal Hematoma: A Rare Presentation. İstanbul Kuzey Klinikleri, Cilt: 5 - Sayı: 1, 60–63. https://ajindex.com/articles/551543

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